A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst

Bibliographic Details
Main Author: Valpaços, Catarina
Publication Date: 2019
Other Authors: Costa, Mariana, Figueiredo, Suzana, Silva, Ana Raquel, Correia-Pinto, Jorge, Osório, Angélica
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://revistas.rcaap.pt/nascercrescer/article/view/12947
Summary: A persistent omphalomesenteric duct is one possible cause of small-bowel volvulus, a rare cause of acute abdomen in children. A four-year-old child was admitted to the Emergency Department with abdominal pain and incoercible vomiting, with neither abdominal guarding nor relevant abnormalities revealed in complementary diagnostic exams. Due to a significant clinical deterioration over a 48-hour observation period, the child was transferred to a tertiary hospital with pediatric surgery. An abdominal ultrasound revealing severe bowel distension and increased abdominal free fluid warranted an exploratory surgery, which identified a voluminous omphalomesenteric duct cyst. When symptomatic, treatment of this condition is consensual and consists of surgical excision of the anatomical abnormality, either by laparoscopy or conventional surgery. The latter was performed. Conclusion: A persistent omphalomesenteric duct is a rare condition that generally requires a high level of clinical suspicion for diagnosis to be made, being most commonly detected during surgery. Associated complications and mortality rates are high, and a timely intervention is key, since surgical removal is the only treatment option.
id RCAP_1f622a2fbec8e85e1fd8bbf68d8ebab2
oai_identifier_str oai:ojs.revistas.rcaap.pt:article/12947
network_acronym_str RCAP
network_name_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository_id_str https://opendoar.ac.uk/repository/7160
spelling A rare case of pediatric volvulus caused by a persistent omphalomesenteric cystUm caso raro de volvo intestinal causado pela persistência de um quisto onfalomesentéricoCase ReportsA persistent omphalomesenteric duct is one possible cause of small-bowel volvulus, a rare cause of acute abdomen in children. A four-year-old child was admitted to the Emergency Department with abdominal pain and incoercible vomiting, with neither abdominal guarding nor relevant abnormalities revealed in complementary diagnostic exams. Due to a significant clinical deterioration over a 48-hour observation period, the child was transferred to a tertiary hospital with pediatric surgery. An abdominal ultrasound revealing severe bowel distension and increased abdominal free fluid warranted an exploratory surgery, which identified a voluminous omphalomesenteric duct cyst. When symptomatic, treatment of this condition is consensual and consists of surgical excision of the anatomical abnormality, either by laparoscopy or conventional surgery. The latter was performed. Conclusion: A persistent omphalomesenteric duct is a rare condition that generally requires a high level of clinical suspicion for diagnosis to be made, being most commonly detected during surgery. Associated complications and mortality rates are high, and a timely intervention is key, since surgical removal is the only treatment option.A persistência do ducto onfalomesentérico pode ser responsável pela formação de um volvo intestinal na porção do intestino delgado, uma causa rara de abdómen agudo em crianças. Uma criança de quatro anos de idade foi admitida no Serviço de Urgência por dor abdominal e vómitos incoercíveis, sem defesa abdominal nem alterações significativas nos exames auxiliares de diagnóstico. Devido a um agravamento clínico significativo no período de 48 horas em que esteve sob observação, foi transferida para um hospital terciário, com acesso a cirurgia pediátrica. Uma nova avaliação ecográfica abdominal, que demonstrou extensa distensão abdominal e presença de líquido livre, levou a exploração cirúrgica, tendo sido identificado e removido um volumoso quisto do canal onfalomesentérico. Quando sintomática, a orientação terapêutica desta patologia é consensual, consistindo na excisão cirúrgica do defeito anatómico, que foi efetuada. Conclusão: A persistência do ducto do canal onfalomesentérico é uma condição rara, cujo diagnóstico exige um elevado nível de suspeição, sendo muitas vezes detetado apenas durante a cirurgia. A taxa de complicações e mortalidade é elevada e uma intervenção atempada é essencial, dado que a remoção cirúrgica constitui a única opção de tratamento.Unidade Local de Saúde de Santo António2019-01-02info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://revistas.rcaap.pt/nascercrescer/article/view/12947eng2183-9417Valpaços, CatarinaCosta, MarianaFigueiredo, SuzanaSilva, Ana RaquelCorreia-Pinto, JorgeOsório, Angélicainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-07T09:43:17Zoai:ojs.revistas.rcaap.pt:article/12947Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:39:37.069239Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
Um caso raro de volvo intestinal causado pela persistência de um quisto onfalomesentérico
title A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
spellingShingle A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
Valpaços, Catarina
Case Reports
title_short A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
title_full A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
title_fullStr A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
title_full_unstemmed A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
title_sort A rare case of pediatric volvulus caused by a persistent omphalomesenteric cyst
author Valpaços, Catarina
author_facet Valpaços, Catarina
Costa, Mariana
Figueiredo, Suzana
Silva, Ana Raquel
Correia-Pinto, Jorge
Osório, Angélica
author_role author
author2 Costa, Mariana
Figueiredo, Suzana
Silva, Ana Raquel
Correia-Pinto, Jorge
Osório, Angélica
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Valpaços, Catarina
Costa, Mariana
Figueiredo, Suzana
Silva, Ana Raquel
Correia-Pinto, Jorge
Osório, Angélica
dc.subject.por.fl_str_mv Case Reports
topic Case Reports
description A persistent omphalomesenteric duct is one possible cause of small-bowel volvulus, a rare cause of acute abdomen in children. A four-year-old child was admitted to the Emergency Department with abdominal pain and incoercible vomiting, with neither abdominal guarding nor relevant abnormalities revealed in complementary diagnostic exams. Due to a significant clinical deterioration over a 48-hour observation period, the child was transferred to a tertiary hospital with pediatric surgery. An abdominal ultrasound revealing severe bowel distension and increased abdominal free fluid warranted an exploratory surgery, which identified a voluminous omphalomesenteric duct cyst. When symptomatic, treatment of this condition is consensual and consists of surgical excision of the anatomical abnormality, either by laparoscopy or conventional surgery. The latter was performed. Conclusion: A persistent omphalomesenteric duct is a rare condition that generally requires a high level of clinical suspicion for diagnosis to be made, being most commonly detected during surgery. Associated complications and mortality rates are high, and a timely intervention is key, since surgical removal is the only treatment option.
publishDate 2019
dc.date.none.fl_str_mv 2019-01-02
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://revistas.rcaap.pt/nascercrescer/article/view/12947
url https://revistas.rcaap.pt/nascercrescer/article/view/12947
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2183-9417
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Unidade Local de Saúde de Santo António
publisher.none.fl_str_mv Unidade Local de Saúde de Santo António
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
_version_ 1833594797208633344