Pediatric idiopathic midgut volvulus and shock in the infant
Main Author: | |
---|---|
Publication Date: | 2020 |
Other Authors: | , , , , , , , , |
Format: | Article |
Language: | eng |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738 |
Summary: | Introduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock. |
id |
RCAP_b1958a62c9c9dee2516acbc55f70ca6d |
---|---|
oai_identifier_str |
oai:ojs.revistas.rcaap.pt:article/18738 |
network_acronym_str |
RCAP |
network_name_str |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
repository_id_str |
https://opendoar.ac.uk/repository/7160 |
spelling |
Pediatric idiopathic midgut volvulus and shock in the infantVólvulo intestinal idiopático e choque no lactenteCase ReportsIntroduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock.Introdução: O vólvulo intestinal é uma emergência cirúrgica que consiste na torção de uma ansa intestinal sobre o seu ponto de inserção, causando obstrução intestinal. Habitualmente apresenta-se com um quadro de vómitos biliares, podendo evoluir para necrose intestinal e choque. Caso Clínico: Um lactente de 40 dias de idade foi observado por inicio súbito de irritabilidade, vómitos biliares, distensão abdominal e hematoquézia. Evoluiu para choque com acidose metabólica e coagulopatia, necessidade de volemização, aminas vasopressoras e ventilação mecânica. Foi submetido a laparotomia, com identificação de vólvulo intestinal sem malrotação e, recuperação da perfusão após desrotação, sem necessidade de resseção intestinal inicial. Após 48 horas, foi submetido a laparotomia de revisão, que demonstrou necrose intestinal com necessidade de enterectomia parcial do intestino delgado. Apesar da gravidade do quadro, o doente apresentou boa evolução clínica. Discussão: A presença de vómitos biliares no lactente é sugestiva de obstrução intestinal. Os autores salientam a presença de vólvulo intestinal sem malrotação, complicado com choque e necrose intestinal.Unidade Local de Saúde de Santo António2020-11-26info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738eng2183-9417Maciel, JulianaSantos, Ana LuisaMarinho, Ana SofiaFigueiredo, SuzanaAraújo, Ana RitaMorgado, HélderLeitão, BanquartSarmento, AlziraFernandes, Sofia RibeiroFerreira, Paula Reginainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-07T09:45:24Zoai:ojs.revistas.rcaap.pt:article/18738Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:39:42.341178Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Pediatric idiopathic midgut volvulus and shock in the infant Vólvulo intestinal idiopático e choque no lactente |
title |
Pediatric idiopathic midgut volvulus and shock in the infant |
spellingShingle |
Pediatric idiopathic midgut volvulus and shock in the infant Maciel, Juliana Case Reports |
title_short |
Pediatric idiopathic midgut volvulus and shock in the infant |
title_full |
Pediatric idiopathic midgut volvulus and shock in the infant |
title_fullStr |
Pediatric idiopathic midgut volvulus and shock in the infant |
title_full_unstemmed |
Pediatric idiopathic midgut volvulus and shock in the infant |
title_sort |
Pediatric idiopathic midgut volvulus and shock in the infant |
author |
Maciel, Juliana |
author_facet |
Maciel, Juliana Santos, Ana Luisa Marinho, Ana Sofia Figueiredo, Suzana Araújo, Ana Rita Morgado, Hélder Leitão, Banquart Sarmento, Alzira Fernandes, Sofia Ribeiro Ferreira, Paula Regina |
author_role |
author |
author2 |
Santos, Ana Luisa Marinho, Ana Sofia Figueiredo, Suzana Araújo, Ana Rita Morgado, Hélder Leitão, Banquart Sarmento, Alzira Fernandes, Sofia Ribeiro Ferreira, Paula Regina |
author2_role |
author author author author author author author author author |
dc.contributor.author.fl_str_mv |
Maciel, Juliana Santos, Ana Luisa Marinho, Ana Sofia Figueiredo, Suzana Araújo, Ana Rita Morgado, Hélder Leitão, Banquart Sarmento, Alzira Fernandes, Sofia Ribeiro Ferreira, Paula Regina |
dc.subject.por.fl_str_mv |
Case Reports |
topic |
Case Reports |
description |
Introduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-11-26 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738 |
url |
https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
2183-9417 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
Unidade Local de Saúde de Santo António |
publisher.none.fl_str_mv |
Unidade Local de Saúde de Santo António |
dc.source.none.fl_str_mv |
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
instname_str |
FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
collection |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
repository.name.fl_str_mv |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
repository.mail.fl_str_mv |
info@rcaap.pt |
_version_ |
1833594798974435328 |