Pediatric idiopathic midgut volvulus and shock in the infant

Bibliographic Details
Main Author: Maciel, Juliana
Publication Date: 2020
Other Authors: Santos, Ana Luisa, Marinho, Ana Sofia, Figueiredo, Suzana, Araújo, Ana Rita, Morgado, Hélder, Leitão, Banquart, Sarmento, Alzira, Fernandes, Sofia Ribeiro, Ferreira, Paula Regina
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738
Summary: Introduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock.
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spelling Pediatric idiopathic midgut volvulus and shock in the infantVólvulo intestinal idiopático e choque no lactenteCase ReportsIntroduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock.Introdução: O vólvulo intestinal é uma emergência cirúrgica que consiste na torção de uma ansa intestinal sobre o seu ponto de inserção, causando obstrução intestinal. Habitualmente apresenta-se com um quadro de vómitos biliares, podendo evoluir para necrose intestinal e choque. Caso Clínico: Um lactente de 40 dias de idade foi observado por inicio súbito de irritabilidade, vómitos biliares, distensão abdominal e hematoquézia. Evoluiu para choque com acidose metabólica e coagulopatia, necessidade de volemização, aminas vasopressoras e ventilação mecânica. Foi submetido a laparotomia, com identificação de vólvulo intestinal sem malrotação e, recuperação da perfusão após desrotação, sem necessidade de resseção intestinal inicial. Após 48 horas, foi submetido a laparotomia de revisão, que demonstrou necrose intestinal com necessidade de enterectomia parcial do intestino delgado. Apesar da gravidade do quadro, o doente apresentou boa evolução clínica. Discussão: A presença de vómitos biliares no lactente é sugestiva de obstrução intestinal. Os autores salientam a presença de vólvulo intestinal sem malrotação, complicado com choque e necrose intestinal.Unidade Local de Saúde de Santo António2020-11-26info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738eng2183-9417Maciel, JulianaSantos, Ana LuisaMarinho, Ana SofiaFigueiredo, SuzanaAraújo, Ana RitaMorgado, HélderLeitão, BanquartSarmento, AlziraFernandes, Sofia RibeiroFerreira, Paula Reginainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-07T09:45:24Zoai:ojs.revistas.rcaap.pt:article/18738Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:39:42.341178Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Pediatric idiopathic midgut volvulus and shock in the infant
Vólvulo intestinal idiopático e choque no lactente
title Pediatric idiopathic midgut volvulus and shock in the infant
spellingShingle Pediatric idiopathic midgut volvulus and shock in the infant
Maciel, Juliana
Case Reports
title_short Pediatric idiopathic midgut volvulus and shock in the infant
title_full Pediatric idiopathic midgut volvulus and shock in the infant
title_fullStr Pediatric idiopathic midgut volvulus and shock in the infant
title_full_unstemmed Pediatric idiopathic midgut volvulus and shock in the infant
title_sort Pediatric idiopathic midgut volvulus and shock in the infant
author Maciel, Juliana
author_facet Maciel, Juliana
Santos, Ana Luisa
Marinho, Ana Sofia
Figueiredo, Suzana
Araújo, Ana Rita
Morgado, Hélder
Leitão, Banquart
Sarmento, Alzira
Fernandes, Sofia Ribeiro
Ferreira, Paula Regina
author_role author
author2 Santos, Ana Luisa
Marinho, Ana Sofia
Figueiredo, Suzana
Araújo, Ana Rita
Morgado, Hélder
Leitão, Banquart
Sarmento, Alzira
Fernandes, Sofia Ribeiro
Ferreira, Paula Regina
author2_role author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Maciel, Juliana
Santos, Ana Luisa
Marinho, Ana Sofia
Figueiredo, Suzana
Araújo, Ana Rita
Morgado, Hélder
Leitão, Banquart
Sarmento, Alzira
Fernandes, Sofia Ribeiro
Ferreira, Paula Regina
dc.subject.por.fl_str_mv Case Reports
topic Case Reports
description Introduction: Intestinal volvulus is a surgical emergency in which a segment of the intestine twists over its mesenteric attachment, causing bowel obstruction. It usually presents with bilious vomiting and can progress to bowel necrosis and shock. Case Report: A 40-days-old male infant presented with acute onset irritability, bilious vomiting, abdominal distention, and hematochezia. He rapidly evolved to shock with metabolic acidosis and coagulopathy, requiring fluid resuscitation, vasoactive agents, and invasive mechanical ventilation. The patient was submitted to urgent laparotomy, confirming midgut volvulus without malrotation. Partial reperfusion of the affected midgut was achieved, with no resection initially performed, but 48 hours later he was re-evaluated and partial enterectomy for midgut necrosis was performed. Despite the condition´s severity, the patient had a good evolution with full recovery. Discussion: Bilious vomiting in the infant is highly suggestive of intestinal obstruction. The authors emphasize the presence of midgut volvulus without malrotation, complicated with bowel necrosis and shock.
publishDate 2020
dc.date.none.fl_str_mv 2020-11-26
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738
url https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18738
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2183-9417
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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dc.publisher.none.fl_str_mv Unidade Local de Saúde de Santo António
publisher.none.fl_str_mv Unidade Local de Saúde de Santo António
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
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instacron_str RCAAP
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reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
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