Mucinous Adenocarcinoma of Skin Annex: a Case Report
Main Author: | |
---|---|
Publication Date: | 2013 |
Other Authors: | , , , |
Format: | Article |
Language: | por |
Source: | Revista Brasileira de Cancerologia (Online) |
DOI: | 10.32635/2176-9745.RBC.2013v59n1.551 |
Download full: | https://rbc.inca.gov.br/index.php/revista/article/view/551 |
Summary: | Introduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common. |
id |
INCA-1_bace934c398e016d7412f5f3ef6bcc0f |
---|---|
oai_identifier_str |
oai:rbc.inca.gov.br:article/551 |
network_acronym_str |
INCA-1 |
network_name_str |
Revista Brasileira de Cancerologia (Online) |
spelling |
Mucinous Adenocarcinoma of Skin Annex: a Case ReportAdenocarcinoma Mucinoso de Anexo Cutáneo: Relato de CasoAdenocarcinoma Mucinoso de Anexo Cutâneo: Relato de CasoFemininoNeoplasiasAdenocarcinoma MucinosoMetástase NeoplásicaRecidivaFemaleNeoplasmsAdenocarcinoma, MucinousNeoplasm MetastasisReccurenceFemeninoNeoplasiasAdenocarcinoma MucinosoMetástasis de la NeoplasiaRecurrenciaIntroduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common. Introducción: El adenocarcinoma mucinoso es una rara neoplasia formada por células apocrinas de la piel híper secretoras de moco. Párpados, cuero cabelludo y otras regiones de la cabeza y el cuello son los sitios primarios más acometidos. Relato del caso: Los autores describen el caso de una lesión sospechosa en el cuero cabelludo, cuya excisión y análisis han confirmado un adenocarcinoma mucinoso. Aún después de la resección, surgieron lesiones metastásicas en las regiones retro auriculares, cervicales, supraclaviculares y cuero cabelludo. Se hizo, entonces, quimioterapia y radioterapia. Meses después, la paciente informó dolor en la columna y en el brazo, con irradiación para la mano y parestesias. Después de las pruebas, se confirmó metástasis en los linfonodos axilares, en los huesos de la columna vertebral, con inminente compresión medular. La radioterapia, entonces fue realizada en estas regiones. La paciente ha presentado una mejoría significativa y mantiene seguimiento. Conclusión: El adenocarcinoma mucinoso es una rara neoplasia y las características del relato presentado lo convierten en aún más rara. El diagnóstico de la enfermedad requiere una correlación clínica, radiológica y patológica. Cuando sometidos a tratamiento precoz, los pacientes presentan un buen pronóstico, con raras posibilidades de metástasis, aunque las recidivas sean comunes. Introdução: O adenocarcinoma mucinoso é uma rara neoplasia formada por células apócrinas da pele hipersecretoras de muco. Pálpebras, couro cabeludo e outras regiões da cabeça e do pescoço são os sítios primários mais acometidos. Relato do caso: Os autores descrevem o caso de uma lesão suspeita em couro cabeludo, cuja excisão e análise confirmaram um adenocarcino mamucinoso de anexo cutâneo. Mesmo após a ressecção, surgiram lesões metastáticas nas regiões retroauricular, cervical, supraclavicular e couro cabeludo. Fez-se, então, quimioterapia e radioterapia. Meses depois, a paciente relatou dor na coluna e no braço com irradiação para a mão e parestesias. Após exames, confirmou-se metástase em linfonodos axilares, em ossos da coluna vertebral, com iminente compressão medular. A radioterapia, então, foi realizada nessas regiões. A paciente apresentou melhora significativa e mantém acompanhamento. Conclusão: O adenocarcinoma mucinoso é uma rara neoplasia e as características do relato apresentado tornam-no ainda mais raro. O diagnóstico da doença exige uma correlação clínica, radiológica e patológica. Quando submetidos a tratamento precoce, os pacientes apresentam um bom prognóstico com raras chances de metástases, embora recidivas sejam comuns. INCA2013-03-29info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/55110.32635/2176-9745.RBC.2013v59n1.551Revista Brasileira de Cancerologia; Vol. 59 No. 1 (2013): Jan./Feb./Mar.; 81-86Revista Brasileira de Cancerologia; Vol. 59 Núm. 1 (2013): ene./feb./mar.; 81-86Revista Brasileira de Cancerologia; v. 59 n. 1 (2013): jan./fev./mar.; 81-862176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/551/338Moura, Karolinny Borinelli de Aquino Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, MartaSantos, Luiz Roberto Medina dos info:eu-repo/semantics/openAccess2021-11-29T20:12:25Zoai:rbc.inca.gov.br:article/551Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T20:12:25Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false |
dc.title.none.fl_str_mv |
Mucinous Adenocarcinoma of Skin Annex: a Case Report Adenocarcinoma Mucinoso de Anexo Cutáneo: Relato de Caso Adenocarcinoma Mucinoso de Anexo Cutâneo: Relato de Caso |
title |
Mucinous Adenocarcinoma of Skin Annex: a Case Report |
spellingShingle |
Mucinous Adenocarcinoma of Skin Annex: a Case Report Mucinous Adenocarcinoma of Skin Annex: a Case Report Moura, Karolinny Borinelli de Aquino Feminino Neoplasias Adenocarcinoma Mucinoso Metástase Neoplásica Recidiva Female Neoplasms Adenocarcinoma, Mucinous Neoplasm Metastasis Reccurence Femenino Neoplasias Adenocarcinoma Mucinoso Metástasis de la Neoplasia Recurrencia Moura, Karolinny Borinelli de Aquino Feminino Neoplasias Adenocarcinoma Mucinoso Metástase Neoplásica Recidiva Female Neoplasms Adenocarcinoma, Mucinous Neoplasm Metastasis Reccurence Femenino Neoplasias Adenocarcinoma Mucinoso Metástasis de la Neoplasia Recurrencia |
title_short |
Mucinous Adenocarcinoma of Skin Annex: a Case Report |
title_full |
Mucinous Adenocarcinoma of Skin Annex: a Case Report |
title_fullStr |
Mucinous Adenocarcinoma of Skin Annex: a Case Report Mucinous Adenocarcinoma of Skin Annex: a Case Report |
title_full_unstemmed |
Mucinous Adenocarcinoma of Skin Annex: a Case Report Mucinous Adenocarcinoma of Skin Annex: a Case Report |
title_sort |
Mucinous Adenocarcinoma of Skin Annex: a Case Report |
author |
Moura, Karolinny Borinelli de Aquino |
author_facet |
Moura, Karolinny Borinelli de Aquino Moura, Karolinny Borinelli de Aquino Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, Marta Santos, Luiz Roberto Medina dos Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, Marta Santos, Luiz Roberto Medina dos |
author_role |
author |
author2 |
Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, Marta Santos, Luiz Roberto Medina dos |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Moura, Karolinny Borinelli de Aquino Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, Marta Santos, Luiz Roberto Medina dos |
dc.subject.por.fl_str_mv |
Feminino Neoplasias Adenocarcinoma Mucinoso Metástase Neoplásica Recidiva Female Neoplasms Adenocarcinoma, Mucinous Neoplasm Metastasis Reccurence Femenino Neoplasias Adenocarcinoma Mucinoso Metástasis de la Neoplasia Recurrencia |
topic |
Feminino Neoplasias Adenocarcinoma Mucinoso Metástase Neoplásica Recidiva Female Neoplasms Adenocarcinoma, Mucinous Neoplasm Metastasis Reccurence Femenino Neoplasias Adenocarcinoma Mucinoso Metástasis de la Neoplasia Recurrencia |
description |
Introduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common. |
publishDate |
2013 |
dc.date.none.fl_str_mv |
2013-03-29 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion Relato de Caso |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rbc.inca.gov.br/index.php/revista/article/view/551 10.32635/2176-9745.RBC.2013v59n1.551 |
url |
https://rbc.inca.gov.br/index.php/revista/article/view/551 |
identifier_str_mv |
10.32635/2176-9745.RBC.2013v59n1.551 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://rbc.inca.gov.br/index.php/revista/article/view/551/338 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
INCA |
publisher.none.fl_str_mv |
INCA |
dc.source.none.fl_str_mv |
Revista Brasileira de Cancerologia; Vol. 59 No. 1 (2013): Jan./Feb./Mar.; 81-86 Revista Brasileira de Cancerologia; Vol. 59 Núm. 1 (2013): ene./feb./mar.; 81-86 Revista Brasileira de Cancerologia; v. 59 n. 1 (2013): jan./fev./mar.; 81-86 2176-9745 reponame:Revista Brasileira de Cancerologia (Online) instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) instacron:INCA |
instname_str |
Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) |
instacron_str |
INCA |
institution |
INCA |
reponame_str |
Revista Brasileira de Cancerologia (Online) |
collection |
Revista Brasileira de Cancerologia (Online) |
repository.name.fl_str_mv |
Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) |
repository.mail.fl_str_mv |
rbc@inca.gov.br |
_version_ |
1822182050591932416 |
dc.identifier.doi.none.fl_str_mv |
10.32635/2176-9745.RBC.2013v59n1.551 |