Mucinous Adenocarcinoma of Skin Annex: a Case Report

Bibliographic Details
Main Author: Moura, Karolinny Borinelli de Aquino
Publication Date: 2013
Other Authors: Dutra, Carolina, Rieg, Carlos Alexandre, Vainchenker, Marta, Santos, Luiz Roberto Medina dos
Format: Article
Language: por
Source: Revista Brasileira de Cancerologia (Online)
DOI: 10.32635/2176-9745.RBC.2013v59n1.551
Download full: https://rbc.inca.gov.br/index.php/revista/article/view/551
Summary: Introduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common.  
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spelling Mucinous Adenocarcinoma of Skin Annex: a Case ReportAdenocarcinoma Mucinoso de Anexo Cutáneo: Relato de CasoAdenocarcinoma Mucinoso de Anexo Cutâneo: Relato de CasoFemininoNeoplasiasAdenocarcinoma MucinosoMetástase NeoplásicaRecidivaFemaleNeoplasmsAdenocarcinoma, MucinousNeoplasm MetastasisReccurenceFemeninoNeoplasiasAdenocarcinoma MucinosoMetástasis de la NeoplasiaRecurrenciaIntroduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common.  Introducción: El adenocarcinoma mucinoso es una rara neoplasia formada por células apocrinas de la piel híper secretoras de moco. Párpados, cuero cabelludo y otras regiones de la cabeza y el cuello son los sitios primarios más acometidos. Relato del caso: Los autores describen el caso de una lesión sospechosa en el cuero cabelludo, cuya excisión y análisis han confirmado un adenocarcinoma mucinoso. Aún después de la resección, surgieron lesiones metastásicas en las regiones retro auriculares, cervicales, supraclaviculares y cuero cabelludo. Se hizo, entonces, quimioterapia y radioterapia. Meses después, la paciente informó dolor en la columna y en el brazo, con irradiación para la mano y parestesias. Después de las pruebas, se confirmó metástasis en los linfonodos axilares, en los huesos de la columna vertebral, con inminente compresión medular. La radioterapia, entonces fue realizada en estas regiones. La paciente ha presentado una mejoría significativa y mantiene seguimiento. Conclusión: El adenocarcinoma mucinoso es una rara neoplasia y las características del relato presentado lo convierten en aún más rara. El diagnóstico de la enfermedad requiere una correlación clínica, radiológica y patológica. Cuando sometidos a tratamiento precoz, los pacientes presentan un buen pronóstico, con raras posibilidades de metástasis, aunque las recidivas sean comunes.  Introdução: O adenocarcinoma mucinoso é uma rara neoplasia formada por células apócrinas da pele hipersecretoras de muco. Pálpebras, couro cabeludo e outras regiões da cabeça e do pescoço são os sítios primários mais acometidos. Relato do caso: Os autores descrevem o caso de uma lesão suspeita em couro cabeludo, cuja excisão e análise confirmaram um adenocarcino mamucinoso de anexo cutâneo. Mesmo após a ressecção, surgiram lesões metastáticas nas regiões retroauricular, cervical, supraclavicular e couro cabeludo. Fez-se, então, quimioterapia e radioterapia. Meses depois, a paciente relatou dor na coluna e no braço com irradiação para a mão e parestesias. Após exames, confirmou-se metástase em linfonodos axilares, em ossos da coluna vertebral, com iminente compressão medular. A radioterapia, então, foi realizada nessas regiões. A paciente apresentou melhora significativa e mantém acompanhamento. Conclusão: O adenocarcinoma mucinoso é uma rara neoplasia e as características do relato apresentado tornam-no ainda mais raro. O diagnóstico da doença exige uma correlação clínica, radiológica e patológica. Quando submetidos a tratamento precoce, os pacientes apresentam um bom prognóstico com raras chances de metástases, embora recidivas sejam comuns.  INCA2013-03-29info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/55110.32635/2176-9745.RBC.2013v59n1.551Revista Brasileira de Cancerologia; Vol. 59 No. 1 (2013): Jan./Feb./Mar.; 81-86Revista Brasileira de Cancerologia; Vol. 59 Núm. 1 (2013): ene./feb./mar.; 81-86Revista Brasileira de Cancerologia; v. 59 n. 1 (2013): jan./fev./mar.; 81-862176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/551/338Moura, Karolinny Borinelli de Aquino Dutra, Carolina Rieg, Carlos Alexandre Vainchenker, MartaSantos, Luiz Roberto Medina dos info:eu-repo/semantics/openAccess2021-11-29T20:12:25Zoai:rbc.inca.gov.br:article/551Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T20:12:25Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Mucinous Adenocarcinoma of Skin Annex: a Case Report
Adenocarcinoma Mucinoso de Anexo Cutáneo: Relato de Caso
Adenocarcinoma Mucinoso de Anexo Cutâneo: Relato de Caso
title Mucinous Adenocarcinoma of Skin Annex: a Case Report
spellingShingle Mucinous Adenocarcinoma of Skin Annex: a Case Report
Mucinous Adenocarcinoma of Skin Annex: a Case Report
Moura, Karolinny Borinelli de Aquino
Feminino
Neoplasias
Adenocarcinoma Mucinoso
Metástase Neoplásica
Recidiva
Female
Neoplasms
Adenocarcinoma, Mucinous
Neoplasm Metastasis
Reccurence
Femenino
Neoplasias
Adenocarcinoma Mucinoso
Metástasis de la Neoplasia
Recurrencia
Moura, Karolinny Borinelli de Aquino
Feminino
Neoplasias
Adenocarcinoma Mucinoso
Metástase Neoplásica
Recidiva
Female
Neoplasms
Adenocarcinoma, Mucinous
Neoplasm Metastasis
Reccurence
Femenino
Neoplasias
Adenocarcinoma Mucinoso
Metástasis de la Neoplasia
Recurrencia
title_short Mucinous Adenocarcinoma of Skin Annex: a Case Report
title_full Mucinous Adenocarcinoma of Skin Annex: a Case Report
title_fullStr Mucinous Adenocarcinoma of Skin Annex: a Case Report
Mucinous Adenocarcinoma of Skin Annex: a Case Report
title_full_unstemmed Mucinous Adenocarcinoma of Skin Annex: a Case Report
Mucinous Adenocarcinoma of Skin Annex: a Case Report
title_sort Mucinous Adenocarcinoma of Skin Annex: a Case Report
author Moura, Karolinny Borinelli de Aquino
author_facet Moura, Karolinny Borinelli de Aquino
Moura, Karolinny Borinelli de Aquino
Dutra, Carolina
Rieg, Carlos Alexandre
Vainchenker, Marta
Santos, Luiz Roberto Medina dos
Dutra, Carolina
Rieg, Carlos Alexandre
Vainchenker, Marta
Santos, Luiz Roberto Medina dos
author_role author
author2 Dutra, Carolina
Rieg, Carlos Alexandre
Vainchenker, Marta
Santos, Luiz Roberto Medina dos
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Moura, Karolinny Borinelli de Aquino
Dutra, Carolina
Rieg, Carlos Alexandre
Vainchenker, Marta
Santos, Luiz Roberto Medina dos
dc.subject.por.fl_str_mv Feminino
Neoplasias
Adenocarcinoma Mucinoso
Metástase Neoplásica
Recidiva
Female
Neoplasms
Adenocarcinoma, Mucinous
Neoplasm Metastasis
Reccurence
Femenino
Neoplasias
Adenocarcinoma Mucinoso
Metástasis de la Neoplasia
Recurrencia
topic Feminino
Neoplasias
Adenocarcinoma Mucinoso
Metástase Neoplásica
Recidiva
Female
Neoplasms
Adenocarcinoma, Mucinous
Neoplasm Metastasis
Reccurence
Femenino
Neoplasias
Adenocarcinoma Mucinoso
Metástasis de la Neoplasia
Recurrencia
description Introduction: The mucinous adenocarcinoma is a rare neoplasm composed of apocrine skin cells that produce mucus. Eyelids, scalp and other regions of the head and neck are the most primary sites affected. Case report: The authors describe a suspicious lesion in the scalp, whose excision and analysis confirmed a mucinous adenocarcinoma of Skin Annex. Even after resection, there were metastatic lesions in these regions: retroauricular, cervical, supraclavicular and scalp. Thus, she went under chemotherapy and radiotherapy. Months later, the patient reported back pain radiating to the arm, hands and paresthesias. After examination, metastases have been confirmed on axillary lymph nodes, bones of the spine, with imminent spinal cord compression. Then, radiation therapy was done in these regions. The patient has improved significantly and, nowadays, she keeps monitoring it. Conclusion: The mucinous adenocarcinoma is a rare neoplasm and the characteristics of this reported case makes it even rarer. The diagnosis requires clinical, radiological and pathological correlation. When the patients are submitted to early treatment, they have a good prognosis with few chances of metastases, although recurrences are common.  
publishDate 2013
dc.date.none.fl_str_mv 2013-03-29
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Relato de Caso
format article
status_str publishedVersion
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10.32635/2176-9745.RBC.2013v59n1.551
url https://rbc.inca.gov.br/index.php/revista/article/view/551
identifier_str_mv 10.32635/2176-9745.RBC.2013v59n1.551
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dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/551/338
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dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 59 No. 1 (2013): Jan./Feb./Mar.; 81-86
Revista Brasileira de Cancerologia; Vol. 59 Núm. 1 (2013): ene./feb./mar.; 81-86
Revista Brasileira de Cancerologia; v. 59 n. 1 (2013): jan./fev./mar.; 81-86
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
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institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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dc.identifier.doi.none.fl_str_mv 10.32635/2176-9745.RBC.2013v59n1.551