Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
Main Author: | |
---|---|
Publication Date: | 2005 |
Other Authors: | , , , , , , , , |
Format: | Article |
Language: | eng |
Source: | Brazilian Journal of Transplantation |
Download full: | https://bjt.emnuvens.com.br/revista/article/view/383 |
Summary: | Introduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list. |
id |
ABTO_b1067aada0a96a6c997542b7996cd3a7 |
---|---|
oai_identifier_str |
oai:ojs3.emnuvens.com.br:article/383 |
network_acronym_str |
ABTO |
network_name_str |
Brazilian Journal of Transplantation |
repository_id_str |
|
spelling |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case reportTRANSPLANTE HEPÁTICO ENTRE VIVOS NO TRATAMENTO DO HEMANGIOENDOTELIOMA EPITELIÓIDE DO FÍGADO – RELATO DE CASOHemangioendothelioma EpithelioidLiverSurgeryTransplantationIntroduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list.Introdução: Hemangioendotelioma epitelióide do fígado é uma neoplasia de origem vascular rara que tem um potencial maligno imprevisível. Cresce em partes moles e ossos, sendo incomum no fígado. Tende a ser multifocal e por isso irresecável. Objetivo: Relatar os resultados do tratamento de uma paciente com hemangioendotelioma epitelióide com transplante de fígado intervivos. Relato de caso: Uma paciente de 39 anos de idade com um imenso hemangioendotelioma epitelióide de fígado, acometendo os segmentos hepáticos III, IV, V, VII e VIII. Como a resposta a tratamentos mais conservadores foi considerada desfavorável, o transplante hepático foi indicado como conduta, sendo o transplante intervivos sugerido. O doador foi o seu irmão de 36 anos de idade, que doou o lobo hepático direito (segmentos V, VI, VII e VIII). O fígado da receptora era grande, de consistência endurecida e sem evidência de nódulos. A técnica utilizada no transplante foi a tradicional técnica de transplante intervivos. A paciente teve uma recuperação excelente, tendo alta hospitalar no 15o dia pós-operatório em uso de MMF, Tacrolimus e corticóides. Conclusão: Transplante em casos de hemangioendotelioma epitelióde de fígado pode ser realizado com altas chances de cura. O transplante intervivos é uma excelente opção para esse grupo de pacientes, que não podem esperar por um fígado na lista de espera pelo órgãoAssociação Brasileira de Transplante de Órgãos (ABTO)2005-09-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://bjt.emnuvens.com.br/revista/article/view/38310.53855/bjt.v8i4.383Brazilian Journal of Transplantation; Vol. 8 No. 4 (2005); 449-451Brazilian Journal of Transplantation; v. 8 n. 4 (2005); 449-4512764-1589reponame:Brazilian Journal of Transplantationinstname:Associação Brasileira de Transplante de Órgãos (ABTO)instacron:ABTOenghttps://bjt.emnuvens.com.br/revista/article/view/383/362Copyright (c) 2021 Brazilian Journal of Transplantationinfo:eu-repo/semantics/openAccessRibeiro Jr, Marcelo A. F.Garcia, Christian EvangelistaSantos, Telma Eugênio dosSilva , Adavio de Oliveira eLeitão , ReginaRibeiro, Cristiane Maria de FreitasFonseca, Alexandre ZanchenkoCambiaghi, Camila de GrandeZantut, Paulo Roberto de ArrudaD’Albuquerque, Luiz Augusto Carneiro2021-09-28T13:46:11Zoai:ojs3.emnuvens.com.br:article/383Revistahttps://bjt.emnuvens.com.br/revistaONGhttps://bjt.emnuvens.com.br/revista/oaibjt@abto.org.brhttps://doi.org/10.53855/2764-15892764-1589opendoar:2021-09-28T13:46:11Brazilian Journal of Transplantation - Associação Brasileira de Transplante de Órgãos (ABTO)false |
dc.title.none.fl_str_mv |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report TRANSPLANTE HEPÁTICO ENTRE VIVOS NO TRATAMENTO DO HEMANGIOENDOTELIOMA EPITELIÓIDE DO FÍGADO – RELATO DE CASO |
title |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
spellingShingle |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report Ribeiro Jr, Marcelo A. F. Hemangioendothelioma Epithelioid Liver Surgery Transplantation |
title_short |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
title_full |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
title_fullStr |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
title_full_unstemmed |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
title_sort |
Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report |
author |
Ribeiro Jr, Marcelo A. F. |
author_facet |
Ribeiro Jr, Marcelo A. F. Garcia, Christian Evangelista Santos, Telma Eugênio dos Silva , Adavio de Oliveira e Leitão , Regina Ribeiro, Cristiane Maria de Freitas Fonseca, Alexandre Zanchenko Cambiaghi, Camila de Grande Zantut, Paulo Roberto de Arruda D’Albuquerque, Luiz Augusto Carneiro |
author_role |
author |
author2 |
Garcia, Christian Evangelista Santos, Telma Eugênio dos Silva , Adavio de Oliveira e Leitão , Regina Ribeiro, Cristiane Maria de Freitas Fonseca, Alexandre Zanchenko Cambiaghi, Camila de Grande Zantut, Paulo Roberto de Arruda D’Albuquerque, Luiz Augusto Carneiro |
author2_role |
author author author author author author author author author |
dc.contributor.author.fl_str_mv |
Ribeiro Jr, Marcelo A. F. Garcia, Christian Evangelista Santos, Telma Eugênio dos Silva , Adavio de Oliveira e Leitão , Regina Ribeiro, Cristiane Maria de Freitas Fonseca, Alexandre Zanchenko Cambiaghi, Camila de Grande Zantut, Paulo Roberto de Arruda D’Albuquerque, Luiz Augusto Carneiro |
dc.subject.por.fl_str_mv |
Hemangioendothelioma Epithelioid Liver Surgery Transplantation |
topic |
Hemangioendothelioma Epithelioid Liver Surgery Transplantation |
description |
Introduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list. |
publishDate |
2005 |
dc.date.none.fl_str_mv |
2005-09-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://bjt.emnuvens.com.br/revista/article/view/383 10.53855/bjt.v8i4.383 |
url |
https://bjt.emnuvens.com.br/revista/article/view/383 |
identifier_str_mv |
10.53855/bjt.v8i4.383 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://bjt.emnuvens.com.br/revista/article/view/383/362 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2021 Brazilian Journal of Transplantation info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2021 Brazilian Journal of Transplantation |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Associação Brasileira de Transplante de Órgãos (ABTO) |
publisher.none.fl_str_mv |
Associação Brasileira de Transplante de Órgãos (ABTO) |
dc.source.none.fl_str_mv |
Brazilian Journal of Transplantation; Vol. 8 No. 4 (2005); 449-451 Brazilian Journal of Transplantation; v. 8 n. 4 (2005); 449-451 2764-1589 reponame:Brazilian Journal of Transplantation instname:Associação Brasileira de Transplante de Órgãos (ABTO) instacron:ABTO |
instname_str |
Associação Brasileira de Transplante de Órgãos (ABTO) |
instacron_str |
ABTO |
institution |
ABTO |
reponame_str |
Brazilian Journal of Transplantation |
collection |
Brazilian Journal of Transplantation |
repository.name.fl_str_mv |
Brazilian Journal of Transplantation - Associação Brasileira de Transplante de Órgãos (ABTO) |
repository.mail.fl_str_mv |
bjt@abto.org.br |
_version_ |
1836111234609446912 |