Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report

Bibliographic Details
Main Author: Ribeiro Jr, Marcelo A. F.
Publication Date: 2005
Other Authors: Garcia, Christian Evangelista, Santos, Telma Eugênio dos, Silva , Adavio de Oliveira e, Leitão , Regina, Ribeiro, Cristiane Maria de Freitas, Fonseca, Alexandre Zanchenko, Cambiaghi, Camila de Grande, Zantut, Paulo Roberto de Arruda, D’Albuquerque, Luiz Augusto Carneiro
Format: Article
Language: eng
Source: Brazilian Journal of Transplantation
Download full: https://bjt.emnuvens.com.br/revista/article/view/383
Summary: Introduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list.
id ABTO_b1067aada0a96a6c997542b7996cd3a7
oai_identifier_str oai:ojs3.emnuvens.com.br:article/383
network_acronym_str ABTO
network_name_str Brazilian Journal of Transplantation
repository_id_str
spelling Living-related liver transplant to treat epithelioid hemangioendothelioma – a case reportTRANSPLANTE HEPÁTICO ENTRE VIVOS NO TRATAMENTO DO HEMANGIOENDOTELIOMA EPITELIÓIDE DO FÍGADO – RELATO DE CASOHemangioendothelioma EpithelioidLiverSurgeryTransplantationIntroduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list.Introdução: Hemangioendotelioma epitelióide do fígado é uma neoplasia de origem vascular rara que tem um potencial maligno imprevisível. Cresce em partes moles e ossos, sendo incomum no fígado. Tende a ser multifocal e por isso irresecável. Objetivo: Relatar os resultados do tratamento de uma paciente com hemangioendotelioma epitelióide com transplante de fígado intervivos. Relato de caso: Uma paciente de 39 anos de idade com um imenso hemangioendotelioma epitelióide de fígado, acometendo os segmentos hepáticos III, IV, V, VII e VIII. Como a resposta a tratamentos mais conservadores foi considerada desfavorável, o transplante hepático foi indicado como conduta, sendo o transplante intervivos sugerido. O doador foi o seu irmão de 36 anos de idade, que doou o lobo hepático direito (segmentos V, VI, VII e VIII). O fígado da receptora era grande, de consistência endurecida e sem evidência de nódulos. A técnica utilizada no transplante foi a tradicional técnica de transplante intervivos. A paciente teve uma recuperação excelente, tendo alta hospitalar no 15o dia pós-operatório em uso de MMF, Tacrolimus e corticóides. Conclusão: Transplante em casos de hemangioendotelioma epitelióde de fígado pode ser realizado com altas chances de cura. O transplante intervivos é uma excelente opção para esse grupo de pacientes, que não podem esperar por um fígado na lista de espera pelo órgãoAssociação Brasileira de Transplante de Órgãos (ABTO)2005-09-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://bjt.emnuvens.com.br/revista/article/view/38310.53855/bjt.v8i4.383Brazilian Journal of Transplantation; Vol. 8 No. 4 (2005); 449-451Brazilian Journal of Transplantation; v. 8 n. 4 (2005); 449-4512764-1589reponame:Brazilian Journal of Transplantationinstname:Associação Brasileira de Transplante de Órgãos (ABTO)instacron:ABTOenghttps://bjt.emnuvens.com.br/revista/article/view/383/362Copyright (c) 2021 Brazilian Journal of Transplantationinfo:eu-repo/semantics/openAccessRibeiro Jr, Marcelo A. F.Garcia, Christian EvangelistaSantos, Telma Eugênio dosSilva , Adavio de Oliveira eLeitão , ReginaRibeiro, Cristiane Maria de FreitasFonseca, Alexandre ZanchenkoCambiaghi, Camila de GrandeZantut, Paulo Roberto de ArrudaD’Albuquerque, Luiz Augusto Carneiro2021-09-28T13:46:11Zoai:ojs3.emnuvens.com.br:article/383Revistahttps://bjt.emnuvens.com.br/revistaONGhttps://bjt.emnuvens.com.br/revista/oaibjt@abto.org.brhttps://doi.org/10.53855/2764-15892764-1589opendoar:2021-09-28T13:46:11Brazilian Journal of Transplantation - Associação Brasileira de Transplante de Órgãos (ABTO)false
dc.title.none.fl_str_mv Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
TRANSPLANTE HEPÁTICO ENTRE VIVOS NO TRATAMENTO DO HEMANGIOENDOTELIOMA EPITELIÓIDE DO FÍGADO – RELATO DE CASO
title Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
spellingShingle Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
Ribeiro Jr, Marcelo A. F.
Hemangioendothelioma Epithelioid
Liver
Surgery
Transplantation
title_short Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
title_full Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
title_fullStr Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
title_full_unstemmed Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
title_sort Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report
author Ribeiro Jr, Marcelo A. F.
author_facet Ribeiro Jr, Marcelo A. F.
Garcia, Christian Evangelista
Santos, Telma Eugênio dos
Silva , Adavio de Oliveira e
Leitão , Regina
Ribeiro, Cristiane Maria de Freitas
Fonseca, Alexandre Zanchenko
Cambiaghi, Camila de Grande
Zantut, Paulo Roberto de Arruda
D’Albuquerque, Luiz Augusto Carneiro
author_role author
author2 Garcia, Christian Evangelista
Santos, Telma Eugênio dos
Silva , Adavio de Oliveira e
Leitão , Regina
Ribeiro, Cristiane Maria de Freitas
Fonseca, Alexandre Zanchenko
Cambiaghi, Camila de Grande
Zantut, Paulo Roberto de Arruda
D’Albuquerque, Luiz Augusto Carneiro
author2_role author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Ribeiro Jr, Marcelo A. F.
Garcia, Christian Evangelista
Santos, Telma Eugênio dos
Silva , Adavio de Oliveira e
Leitão , Regina
Ribeiro, Cristiane Maria de Freitas
Fonseca, Alexandre Zanchenko
Cambiaghi, Camila de Grande
Zantut, Paulo Roberto de Arruda
D’Albuquerque, Luiz Augusto Carneiro
dc.subject.por.fl_str_mv Hemangioendothelioma Epithelioid
Liver
Surgery
Transplantation
topic Hemangioendothelioma Epithelioid
Liver
Surgery
Transplantation
description Introduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list.
publishDate 2005
dc.date.none.fl_str_mv 2005-09-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://bjt.emnuvens.com.br/revista/article/view/383
10.53855/bjt.v8i4.383
url https://bjt.emnuvens.com.br/revista/article/view/383
identifier_str_mv 10.53855/bjt.v8i4.383
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://bjt.emnuvens.com.br/revista/article/view/383/362
dc.rights.driver.fl_str_mv Copyright (c) 2021 Brazilian Journal of Transplantation
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2021 Brazilian Journal of Transplantation
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Associação Brasileira de Transplante de Órgãos (ABTO)
publisher.none.fl_str_mv Associação Brasileira de Transplante de Órgãos (ABTO)
dc.source.none.fl_str_mv Brazilian Journal of Transplantation; Vol. 8 No. 4 (2005); 449-451
Brazilian Journal of Transplantation; v. 8 n. 4 (2005); 449-451
2764-1589
reponame:Brazilian Journal of Transplantation
instname:Associação Brasileira de Transplante de Órgãos (ABTO)
instacron:ABTO
instname_str Associação Brasileira de Transplante de Órgãos (ABTO)
instacron_str ABTO
institution ABTO
reponame_str Brazilian Journal of Transplantation
collection Brazilian Journal of Transplantation
repository.name.fl_str_mv Brazilian Journal of Transplantation - Associação Brasileira de Transplante de Órgãos (ABTO)
repository.mail.fl_str_mv bjt@abto.org.br
_version_ 1836111234609446912