Loeys-Dietz Syndrome and pregnancy: two case reports and literature review

Detalhes bibliográficos
Autor(a) principal: Vargas,Sara
Data de Publicação: 2020
Outros Autores: Moldovan,Oana, Lança,Filipa, Centeno,Mónica, Pinto,Luísa
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Texto Completo: http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263
Resumo: Abstract Loeys-Dietz syndrome is a rare autosomal dominant connective tissue disorder characterized by vascular, skeletal, craniofacial and cutaneous abnormalities. During pregnancy, women with this syndrome have an increased risk of aortic aneurysm and dissection, preterm birth, uterine rupture and postpartum hemorrhage. Appropriate preconceptional, pregnancy and postpartum evaluation, counseling and surveillance by a specialized and multidisciplinary team might improve maternal and pregnancy outcomes. We present two cases of pregnant women with this syndrome surveilled at a tertiary high-risk obstetrics center. Both delivered at term without major complications.
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spelling Loeys-Dietz Syndrome and pregnancy: two case reports and literature reviewPregnancyCardiovascular DiseasesLoeys-Dietz SyndromePregnancy ComplicationsAbstract Loeys-Dietz syndrome is a rare autosomal dominant connective tissue disorder characterized by vascular, skeletal, craniofacial and cutaneous abnormalities. During pregnancy, women with this syndrome have an increased risk of aortic aneurysm and dissection, preterm birth, uterine rupture and postpartum hemorrhage. Appropriate preconceptional, pregnancy and postpartum evaluation, counseling and surveillance by a specialized and multidisciplinary team might improve maternal and pregnancy outcomes. We present two cases of pregnant women with this syndrome surveilled at a tertiary high-risk obstetrics center. Both delivered at term without major complications.Euromédice, Edições Médicas Lda.2020-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263Acta Obstétrica e Ginecológica Portuguesa v.14 n.4 2020reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263Vargas,SaraMoldovan,OanaLança,FilipaCenteno,MónicaPinto,Luísainfo:eu-repo/semantics/openAccess2024-02-06T17:21:50Zoai:scielo:S1646-58302020000400263Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T13:09:12.524238Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
title Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
spellingShingle Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
Vargas,Sara
Pregnancy
Cardiovascular Diseases
Loeys-Dietz Syndrome
Pregnancy Complications
title_short Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
title_full Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
title_fullStr Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
title_full_unstemmed Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
title_sort Loeys-Dietz Syndrome and pregnancy: two case reports and literature review
author Vargas,Sara
author_facet Vargas,Sara
Moldovan,Oana
Lança,Filipa
Centeno,Mónica
Pinto,Luísa
author_role author
author2 Moldovan,Oana
Lança,Filipa
Centeno,Mónica
Pinto,Luísa
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Vargas,Sara
Moldovan,Oana
Lança,Filipa
Centeno,Mónica
Pinto,Luísa
dc.subject.por.fl_str_mv Pregnancy
Cardiovascular Diseases
Loeys-Dietz Syndrome
Pregnancy Complications
topic Pregnancy
Cardiovascular Diseases
Loeys-Dietz Syndrome
Pregnancy Complications
description Abstract Loeys-Dietz syndrome is a rare autosomal dominant connective tissue disorder characterized by vascular, skeletal, craniofacial and cutaneous abnormalities. During pregnancy, women with this syndrome have an increased risk of aortic aneurysm and dissection, preterm birth, uterine rupture and postpartum hemorrhage. Appropriate preconceptional, pregnancy and postpartum evaluation, counseling and surveillance by a specialized and multidisciplinary team might improve maternal and pregnancy outcomes. We present two cases of pregnant women with this syndrome surveilled at a tertiary high-risk obstetrics center. Both delivered at term without major complications.
publishDate 2020
dc.date.none.fl_str_mv 2020-12-01
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263
url http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302020000400263
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Euromédice, Edições Médicas Lda.
publisher.none.fl_str_mv Euromédice, Edições Médicas Lda.
dc.source.none.fl_str_mv Acta Obstétrica e Ginecológica Portuguesa v.14 n.4 2020
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
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instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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