MRI Findings in Rasmussen’s Encephalitis
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Publication Date: | 2012 |
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Format: | Article |
Language: | por |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276 |
Summary: | Introduction: Rasmussen’s encephalitis is a chronic inflammatory encephalitis of unknown etiology. Clinical, imaging and electroencephalographic characteristic findings allow its diagnosis. Serial brain MRI evaluation of these patients has a characteristic pattern of temporal evolution. Regarding a clinical case, the authors make a brief review of this pathology, with particular emphasis on the MRI findings. Case Report: Female child, seven years old, who started a drug-resistent focal epilepsy at the age of four. The video-EEG revealed a left fronto-temporal epileptogenic focus. The serial MRI evaluation showed a left fronto-temporal and insular lesion with variation of its imaging features over time. After thorough investigation, the diagnosis of exclusion was that of Rasmussen’s encephalitis. Conclusion: MRI plays an important role in the diagnosis and monitoring of Rasmussen’s encephalitis. Regarding a clinical case, we review this pathology, specially its MRI findings. |
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MRI Findings in Rasmussen’s EncephalitisAchados em Ressonância Magnética na Encefalite de RasmussenIntroduction: Rasmussen’s encephalitis is a chronic inflammatory encephalitis of unknown etiology. Clinical, imaging and electroencephalographic characteristic findings allow its diagnosis. Serial brain MRI evaluation of these patients has a characteristic pattern of temporal evolution. Regarding a clinical case, the authors make a brief review of this pathology, with particular emphasis on the MRI findings. Case Report: Female child, seven years old, who started a drug-resistent focal epilepsy at the age of four. The video-EEG revealed a left fronto-temporal epileptogenic focus. The serial MRI evaluation showed a left fronto-temporal and insular lesion with variation of its imaging features over time. After thorough investigation, the diagnosis of exclusion was that of Rasmussen’s encephalitis. Conclusion: MRI plays an important role in the diagnosis and monitoring of Rasmussen’s encephalitis. Regarding a clinical case, we review this pathology, specially its MRI findings.Introdução: A encefalite de Rasmussen é uma encefalite crónica e progressiva, de etiologia desconhecida. Achados clínicos, imagiológicos e electroencefalográficos característicos permitem o seu diagnóstico. Na avaliação seriada destes doentes por ressonância magnétcia (RM) crânio-encefálica está descrito um padrão imagiológico típico de evolução temporal. A propósito de um caso clínico, os autores fazem uma breve revisão desta patologia, enfatizando os achados em RM. Caso Clínico: Criança do sexo feminino, com sete anos de idade, que aos quatro anos inicia uma epilepsia focal refractária à terapêutica, com vídeo-EEG mostrando um foco epileptogénico fronto-temporal esquerdo. A avaliação seriada por RM mostrou lesão frontotemporo-insular esquerda, com flutuação das suas características imagiológicas ao longo do tempo. Após investigação aprofundada, o diagnóstico de exclusão foi o de encefalite de Rasmussen. Conclusão: A RM crânio-encefálica desempenha um importante papel no diagnóstico e seguimento da encefalite de Rasmussen. A propósito de um caso clínico, é revista esta patologia, particularmente os seus achados em RM.Ordem dos Médicos2012-11-02info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/x-pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276oai:ojs.www.actamedicaportuguesa.com:article/276Acta Médica Portuguesa; Vol. 25 (2012): Supplement 1; 68-72Acta Médica Portuguesa; Vol. 25 (2012): Suplemento 1; 68-721646-07580870-399Xreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276/77Mendes Dos Santos, CarolinaMoreno, TeresaSá, GraçaRodrigues, DavidCampos, Jorge Ginfo:eu-repo/semantics/openAccess2022-12-20T10:55:57Zoai:ojs.www.actamedicaportuguesa.com:article/276Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:36:13.225681Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
MRI Findings in Rasmussen’s Encephalitis Achados em Ressonância Magnética na Encefalite de Rasmussen |
title |
MRI Findings in Rasmussen’s Encephalitis |
spellingShingle |
MRI Findings in Rasmussen’s Encephalitis Mendes Dos Santos, Carolina |
title_short |
MRI Findings in Rasmussen’s Encephalitis |
title_full |
MRI Findings in Rasmussen’s Encephalitis |
title_fullStr |
MRI Findings in Rasmussen’s Encephalitis |
title_full_unstemmed |
MRI Findings in Rasmussen’s Encephalitis |
title_sort |
MRI Findings in Rasmussen’s Encephalitis |
author |
Mendes Dos Santos, Carolina |
author_facet |
Mendes Dos Santos, Carolina Moreno, Teresa Sá, Graça Rodrigues, David Campos, Jorge G |
author_role |
author |
author2 |
Moreno, Teresa Sá, Graça Rodrigues, David Campos, Jorge G |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Mendes Dos Santos, Carolina Moreno, Teresa Sá, Graça Rodrigues, David Campos, Jorge G |
description |
Introduction: Rasmussen’s encephalitis is a chronic inflammatory encephalitis of unknown etiology. Clinical, imaging and electroencephalographic characteristic findings allow its diagnosis. Serial brain MRI evaluation of these patients has a characteristic pattern of temporal evolution. Regarding a clinical case, the authors make a brief review of this pathology, with particular emphasis on the MRI findings. Case Report: Female child, seven years old, who started a drug-resistent focal epilepsy at the age of four. The video-EEG revealed a left fronto-temporal epileptogenic focus. The serial MRI evaluation showed a left fronto-temporal and insular lesion with variation of its imaging features over time. After thorough investigation, the diagnosis of exclusion was that of Rasmussen’s encephalitis. Conclusion: MRI plays an important role in the diagnosis and monitoring of Rasmussen’s encephalitis. Regarding a clinical case, we review this pathology, specially its MRI findings. |
publishDate |
2012 |
dc.date.none.fl_str_mv |
2012-11-02 |
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info:eu-repo/semantics/publishedVersion |
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info:eu-repo/semantics/article |
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article |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276 oai:ojs.www.actamedicaportuguesa.com:article/276 |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276 |
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oai:ojs.www.actamedicaportuguesa.com:article/276 |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276/77 |
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Ordem dos Médicos |
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Ordem dos Médicos |
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Acta Médica Portuguesa; Vol. 25 (2012): Supplement 1; 68-72 Acta Médica Portuguesa; Vol. 25 (2012): Suplemento 1; 68-72 1646-0758 0870-399X reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
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