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OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent

Bibliographic Details
Main Author: Antunes, Joana
Publication Date: 2019
Other Authors: Barros, Mariana, Ezequiel, Marta, Calado, Rita, Martins, Mafalda
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.25754/pjp.2019.14892
Summary: OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who
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spelling OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an AdolescentSíndrome OHVIRACase reportsOHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis whoA Síndrome OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) ou Síndrome de Herlyn-Werner-Wunderlich é uma doença congénita rara, secundária a uma anomalia mulleriana, caracterizada por útero didelfos, obstrução da hemivagina e agenésia renal ipsilateral. Apresenta-se habitualmente após a menarca com dor abdominal progressiva e tumefação pélvica secundárias a hematocolpus. Quando a obstrução da hemivagina não é completa o diagnóstico pode ser atrasado pela diminuição da gravidade dos sintomas e possível regularidade do ciclo menstrual. Raramente, surge na idade adulta como causa de infertilidade primária. É descrito um caso de uma adolescente de 15 anos, com diagnóstico pré-natal de agenésia renal direita com queixas de dor abdominal recorrente associada a tumefação abdomino-pélvica.Sociedade Portuguesa de Pediatria2019-07-15info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25754/pjp.2019.14892eng2184-44532184-3333Antunes, JoanaBarros, MarianaEzequiel, MartaCalado, RitaMartins, Mafaldainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-06T15:12:14Zoai:ojs.revistas.rcaap.pt:article/14892Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:38:36.568931Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
Síndrome OHVIRA
title OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
spellingShingle OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
Antunes, Joana
Case reports
title_short OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_full OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_fullStr OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_full_unstemmed OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_sort OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
author Antunes, Joana
author_facet Antunes, Joana
Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
author_role author
author2 Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Antunes, Joana
Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
dc.subject.por.fl_str_mv Case reports
topic Case reports
description OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who
publishDate 2019
dc.date.none.fl_str_mv 2019-07-15
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.25754/pjp.2019.14892
url https://doi.org/10.25754/pjp.2019.14892
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2184-4453
2184-3333
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
_version_ 1833594781745283072

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