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Gallbladder Agenesis: A Case Report of an intraoperative diagnosis

Bibliographic Details
Main Author: Carvalho, Ana Cristina Silva
Publication Date: 2017
Other Authors: Santos Costa, Carlos, Correia, Pinto, Magalhães, Jorge, Brito, Diana, Martins, Marta da Cruz, Longras, Catarina, Santos, Teresa, Castro, Vânia, Oliveira, Juliana
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://revista.spcir.com/index.php/spcir/article/view/605
Summary: Introduction: Agenesis of the gallbladder is a rare congenital anomaly occurring in 10 to 65 per 100 000 people. Patients are usually asymptomatic and the diagnosis is made as an incidental finding during another abdominal surgery or at autopsy. The presence of biliary symptoms and a misleading ultrasound study can lead to unnecessary surgery. Case Presentation: We present a 43-year-old female proposed to laparoscopic cholecystectomy for suspected symptomatic gallbladder lithiasis in the clinical and radiological studies prior to surgery. During operation the gallbladder was not identified and the procedure was terminated for further diagnostic procedures. The post-operative study with magnetic resonance cholangiopancreatography confirmed the diagnosis of gallbladder agenesis. Conclusion: The difficulty in diagnosing the absence of gallbladder in the preoperative period can be explained by the infrequency of the condition and consequent low index of suspicion for agenesis when interpreting imaging findings. Surgeons must be aware of this condition and when gallbladder isn’t visualized at laparoscopy decide between convert surgery to open procedure or abort surgery and continue study with other imaging techniques. The latter is a good option, allowing a better characterization of biliary anatomy as well as avoiding morbidity of a laparotomy.
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spelling Gallbladder Agenesis: A Case Report of an intraoperative diagnosisAgenesia da Vesícula Biliar: Relato de Caso de um diagnóstico intra-operatórioGallbladderagenesislaparoscopic cholecystectomycase reportgallbladderagenesislaparoscopic cholecystectomyvesícula biliaragenesiacolecistectomia laparoscópicacaso clínicoIntroduction: Agenesis of the gallbladder is a rare congenital anomaly occurring in 10 to 65 per 100 000 people. Patients are usually asymptomatic and the diagnosis is made as an incidental finding during another abdominal surgery or at autopsy. The presence of biliary symptoms and a misleading ultrasound study can lead to unnecessary surgery. Case Presentation: We present a 43-year-old female proposed to laparoscopic cholecystectomy for suspected symptomatic gallbladder lithiasis in the clinical and radiological studies prior to surgery. During operation the gallbladder was not identified and the procedure was terminated for further diagnostic procedures. The post-operative study with magnetic resonance cholangiopancreatography confirmed the diagnosis of gallbladder agenesis. Conclusion: The difficulty in diagnosing the absence of gallbladder in the preoperative period can be explained by the infrequency of the condition and consequent low index of suspicion for agenesis when interpreting imaging findings. Surgeons must be aware of this condition and when gallbladder isn’t visualized at laparoscopy decide between convert surgery to open procedure or abort surgery and continue study with other imaging techniques. The latter is a good option, allowing a better characterization of biliary anatomy as well as avoiding morbidity of a laparotomy.Introdução: A agenesia da vesícula biliar é uma anomalia congénita rara que ocorre em 10-65/100 000 pessoas. Os doentes são geralmente assintomáticos e o diagnóstico é feito como um achado incidental durante outra cirurgia abdominal ou na autópsia. A existência de sintomatologia biliar e uma ecografia não esclarecedora podem ser a causa de uma cirurgia desnecessária. Caso Clínico: apresentamos o caso de mulher de 43 anos proposta para colecistectomia laparoscópica por suspeita de litíase biliar sintomática na avaliação clinica e radiológica prévia à cirurgia. No intra-operatório a vesícula biliar não foi identificada e terminou-se a cirurgia para execução de outros procedimentos diagnósticos. O estudo pós-operatório com Colangiorressonância confirmou o diagnóstico de agenesia da vesícula biliar. Conclusão: A dificuldade no diagnóstico de agenesia da vesícula biliar no período pré-operatório pode ser explicada pela raridade da situação e consequente baixo índice de suspeição ao interpretar os achados imagiológicos. Os cirurgiões devem conhecer esta entidade e quando a vesícula biliar não se visualiza na laparoscopia, decidir entre a conversão do procedimento ou terminar a cirurgia e continuar o estudo com outros meios imagiológicos. Esta parece ser uma boa opção, permitindo não só uma boa caracterização da anatomia biliar como evitar a morbilidade de uma laparotomia.Sociedade Portuguesa de Cirurgia2017-12-31info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://revista.spcir.com/index.php/spcir/article/view/605Revista Portuguesa de Cirurgia; No. 43 (2017): Number 43 - December 2017; 29 - 32Revista Portuguesa de Cirurgia; N.º 43 (2017): Número 43 - Dezembro 2017; 29 - 322183-11651646-6918reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPenghttps://revista.spcir.com/index.php/spcir/article/view/605https://revista.spcir.com/index.php/spcir/article/view/605/517Copyright (c) 2017 Revista Portuguesa de Cirurgiainfo:eu-repo/semantics/openAccessCarvalho, Ana Cristina SilvaSantos Costa, CarlosCorreia, PintoMagalhães, JorgeBrito, DianaMartins, Marta da CruzLongras, CatarinaSantos, TeresaCastro, VâniaOliveira, Juliana2024-10-24T16:53:05Zoai:revista.spcir.com:article/605Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T19:00:39.991489Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
Agenesia da Vesícula Biliar: Relato de Caso de um diagnóstico intra-operatório
title Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
spellingShingle Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
Carvalho, Ana Cristina Silva
Gallbladder
agenesis
laparoscopic cholecystectomy
case report
gallbladder
agenesis
laparoscopic cholecystectomy
vesícula biliar
agenesia
colecistectomia laparoscópica
caso clínico
title_short Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
title_full Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
title_fullStr Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
title_full_unstemmed Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
title_sort Gallbladder Agenesis: A Case Report of an intraoperative diagnosis
author Carvalho, Ana Cristina Silva
author_facet Carvalho, Ana Cristina Silva
Santos Costa, Carlos
Correia, Pinto
Magalhães, Jorge
Brito, Diana
Martins, Marta da Cruz
Longras, Catarina
Santos, Teresa
Castro, Vânia
Oliveira, Juliana
author_role author
author2 Santos Costa, Carlos
Correia, Pinto
Magalhães, Jorge
Brito, Diana
Martins, Marta da Cruz
Longras, Catarina
Santos, Teresa
Castro, Vânia
Oliveira, Juliana
author2_role author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Carvalho, Ana Cristina Silva
Santos Costa, Carlos
Correia, Pinto
Magalhães, Jorge
Brito, Diana
Martins, Marta da Cruz
Longras, Catarina
Santos, Teresa
Castro, Vânia
Oliveira, Juliana
dc.subject.por.fl_str_mv Gallbladder
agenesis
laparoscopic cholecystectomy
case report
gallbladder
agenesis
laparoscopic cholecystectomy
vesícula biliar
agenesia
colecistectomia laparoscópica
caso clínico
topic Gallbladder
agenesis
laparoscopic cholecystectomy
case report
gallbladder
agenesis
laparoscopic cholecystectomy
vesícula biliar
agenesia
colecistectomia laparoscópica
caso clínico
description Introduction: Agenesis of the gallbladder is a rare congenital anomaly occurring in 10 to 65 per 100 000 people. Patients are usually asymptomatic and the diagnosis is made as an incidental finding during another abdominal surgery or at autopsy. The presence of biliary symptoms and a misleading ultrasound study can lead to unnecessary surgery. Case Presentation: We present a 43-year-old female proposed to laparoscopic cholecystectomy for suspected symptomatic gallbladder lithiasis in the clinical and radiological studies prior to surgery. During operation the gallbladder was not identified and the procedure was terminated for further diagnostic procedures. The post-operative study with magnetic resonance cholangiopancreatography confirmed the diagnosis of gallbladder agenesis. Conclusion: The difficulty in diagnosing the absence of gallbladder in the preoperative period can be explained by the infrequency of the condition and consequent low index of suspicion for agenesis when interpreting imaging findings. Surgeons must be aware of this condition and when gallbladder isn’t visualized at laparoscopy decide between convert surgery to open procedure or abort surgery and continue study with other imaging techniques. The latter is a good option, allowing a better characterization of biliary anatomy as well as avoiding morbidity of a laparotomy.
publishDate 2017
dc.date.none.fl_str_mv 2017-12-31
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://revista.spcir.com/index.php/spcir/article/view/605
url https://revista.spcir.com/index.php/spcir/article/view/605
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://revista.spcir.com/index.php/spcir/article/view/605
https://revista.spcir.com/index.php/spcir/article/view/605/517
dc.rights.driver.fl_str_mv Copyright (c) 2017 Revista Portuguesa de Cirurgia
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2017 Revista Portuguesa de Cirurgia
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
dc.source.none.fl_str_mv Revista Portuguesa de Cirurgia; No. 43 (2017): Number 43 - December 2017; 29 - 32
Revista Portuguesa de Cirurgia; N.º 43 (2017): Número 43 - Dezembro 2017; 29 - 32
2183-1165
1646-6918
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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