PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD
Autor(a) principal: | |
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Data de Publicação: | 2013 |
Outros Autores: | |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Texto Completo: | https://doi.org/10.29021/spdv.70.2.23 |
Resumo: | The systemic vasculitis are a group of diseases, uncommon in childhood, characterized by inflammation and necrosis. Its heterogeneous clinical presentation is conditioned by the type of vessel and organ affected. Recently it was proposed a classification of pediatric vasculitis, which takes into account the size of the vessels involved, and also validated diagnostic criteria for the types most common in children. This review aims to address the most frequent types of vasculitis in childhood, clinical manifestations, diagnosis and therapy.KEYWORDS – Vasculitis; Child. |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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PRIMARY SYSTEMIC VASCULITIS IN CHILDHOODVASCULITES SISTÉMICAS PRIMÁRIAS DA INFÂNCIAThe systemic vasculitis are a group of diseases, uncommon in childhood, characterized by inflammation and necrosis. Its heterogeneous clinical presentation is conditioned by the type of vessel and organ affected. Recently it was proposed a classification of pediatric vasculitis, which takes into account the size of the vessels involved, and also validated diagnostic criteria for the types most common in children. This review aims to address the most frequent types of vasculitis in childhood, clinical manifestations, diagnosis and therapy.KEYWORDS – Vasculitis; Child.As vasculites sistémicas constituem um grupo de doenças, pouco frequentes na infância, caracterizadas por inflamação e necrose vascular. A sua tradução clínica é heterogénea, condicionada pelo tipo de vaso e orgão afectados. Recentemente foi proposta uma classificação das vasculites em idade pediátrica, que tem em conta a dimensão dos vasos envolvidos, sendo também validados critérios de diagnóstico para os tipos mais frequentes em crianças. A presente revisão tem como objectivo abordar os tipos mais frequentes de vasculites na infância, suas ma- nifestações clínicas, diagnóstico e terapêutica.PALAVRAS-CHAVE – Vasculites; Criança.Sociedade Portuguesa de Dermatologia e Venereologia2013-01-17T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.70.2.23oai:ojs.revista.spdv.com.pt:article/23Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 2 (2012): Abril - Junho; 173Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 2 (2012): Abril - Junho; 1732182-24092182-2395reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/23https://doi.org/10.29021/spdv.70.2.23https://revista.spdv.com.pt/index.php/spdv/article/view/23/23Pereira, NádiaAmaro, Cristinainfo:eu-repo/semantics/openAccess2022-10-06T12:34:35Zoai:ojs.revista.spdv.com.pt:article/23Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:30:30.520682Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD VASCULITES SISTÉMICAS PRIMÁRIAS DA INFÂNCIA |
title |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
spellingShingle |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD Pereira, Nádia |
title_short |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
title_full |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
title_fullStr |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
title_full_unstemmed |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
title_sort |
PRIMARY SYSTEMIC VASCULITIS IN CHILDHOOD |
author |
Pereira, Nádia |
author_facet |
Pereira, Nádia Amaro, Cristina |
author_role |
author |
author2 |
Amaro, Cristina |
author2_role |
author |
dc.contributor.author.fl_str_mv |
Pereira, Nádia Amaro, Cristina |
description |
The systemic vasculitis are a group of diseases, uncommon in childhood, characterized by inflammation and necrosis. Its heterogeneous clinical presentation is conditioned by the type of vessel and organ affected. Recently it was proposed a classification of pediatric vasculitis, which takes into account the size of the vessels involved, and also validated diagnostic criteria for the types most common in children. This review aims to address the most frequent types of vasculitis in childhood, clinical manifestations, diagnosis and therapy.KEYWORDS – Vasculitis; Child. |
publishDate |
2013 |
dc.date.none.fl_str_mv |
2013-01-17T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.70.2.23 oai:ojs.revista.spdv.com.pt:article/23 |
url |
https://doi.org/10.29021/spdv.70.2.23 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/23 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/23 https://doi.org/10.29021/spdv.70.2.23 https://revista.spdv.com.pt/index.php/spdv/article/view/23/23 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 2 (2012): Abril - Junho; 173 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 2 (2012): Abril - Junho; 173 2182-2409 2182-2395 reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
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FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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RCAAP |
institution |
RCAAP |
reponame_str |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
collection |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
repository.name.fl_str_mv |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
repository.mail.fl_str_mv |
info@rcaap.pt |
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