LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME

Bibliographic Details
Main Author: Sabia, Lívia Mendes
Publication Date: 2014
Other Authors: Elias, Beatriz Lopes, Lessa, Priscila Pacheco, Ferreira, Flávia Regina, de Lira, Márcia Lanzoni Alvarenga, Mandelbaum, Samuel Henrique
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.29021/spdv.72.2.261
Summary: Lassueur Graham-Little-Piccardi syndrome is a rare dermatosis of unknown etiology that affects mainly women between 30 and 60 years old. It is characterized by the triad of multifocal scarring alopecia of the scalp, lichenoid follicular eruption and hypotrichosis of axillary and pubic regions. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. Therapy is a challenge, with frequent relapses after local and systemic treatments. We report a typical case of this rare syndrome in a male patient of 46 years.
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spelling LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROMESÍNDROME DE GRAHAM-LITTLE-PICCARDI-LASSUEURAlopeciaHypotrichosisLichen planusAlopeciaHipotricoseLíquen planoLassueur Graham-Little-Piccardi syndrome is a rare dermatosis of unknown etiology that affects mainly women between 30 and 60 years old. It is characterized by the triad of multifocal scarring alopecia of the scalp, lichenoid follicular eruption and hypotrichosis of axillary and pubic regions. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. Therapy is a challenge, with frequent relapses after local and systemic treatments. We report a typical case of this rare syndrome in a male patient of 46 years.Síndrome de Graham-Little-Piccardi-Lassueur (SGLPL) é uma dermatose rara, de etiologia desconhecida, que acomete principalmente mulheres entre 30 a 60 anos de idade. Caracteriza-se pela tríade de alopecia cicatricial multifocal do couro cabeludo, erupção folicular liquenoide e hipotricose das regiões axilar e pubiana. O exame anatomopatológico revela diminuição do numero dos folículos pilosos, infiltrado perifolicular e fibrose. A terapêutica é um desafio, com recidivas frequentes após tratamentos locais e sistêmicos. Relatamos um caso típico desta síndrome rara, em um paciente sexo masculino de 46 anos.Sociedade Portuguesa de Dermatologia e Venereologia2014-09-19T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.72.2.261oai:ojs.revista.spdv.com.pt:article/261Journal of the Portuguese Society of Dermatology and Venereology; Vol 72 No 2 (2014): Abril - Junho; 233-235Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 72 n. 2 (2014): Abril - Junho; 233-2352182-24092182-2395reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/261https://doi.org/10.29021/spdv.72.2.261https://revista.spdv.com.pt/index.php/spdv/article/view/261/236Sabia, Lívia MendesElias, Beatriz LopesLessa, Priscila PachecoFerreira, Flávia Reginade Lira, Márcia Lanzoni AlvarengaMandelbaum, Samuel Henriqueinfo:eu-repo/semantics/openAccess2022-10-06T12:34:48Zoai:ojs.revista.spdv.com.pt:article/261Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:31:00.961465Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
SÍNDROME DE GRAHAM-LITTLE-PICCARDI-LASSUEUR
title LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
spellingShingle LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
Sabia, Lívia Mendes
Alopecia
Hypotrichosis
Lichen planus
Alopecia
Hipotricose
Líquen plano
title_short LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
title_full LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
title_fullStr LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
title_full_unstemmed LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
title_sort LASSUER -GRAHAM-LITTLE-PICCARDI SYNDROME
author Sabia, Lívia Mendes
author_facet Sabia, Lívia Mendes
Elias, Beatriz Lopes
Lessa, Priscila Pacheco
Ferreira, Flávia Regina
de Lira, Márcia Lanzoni Alvarenga
Mandelbaum, Samuel Henrique
author_role author
author2 Elias, Beatriz Lopes
Lessa, Priscila Pacheco
Ferreira, Flávia Regina
de Lira, Márcia Lanzoni Alvarenga
Mandelbaum, Samuel Henrique
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Sabia, Lívia Mendes
Elias, Beatriz Lopes
Lessa, Priscila Pacheco
Ferreira, Flávia Regina
de Lira, Márcia Lanzoni Alvarenga
Mandelbaum, Samuel Henrique
dc.subject.por.fl_str_mv Alopecia
Hypotrichosis
Lichen planus
Alopecia
Hipotricose
Líquen plano
topic Alopecia
Hypotrichosis
Lichen planus
Alopecia
Hipotricose
Líquen plano
description Lassueur Graham-Little-Piccardi syndrome is a rare dermatosis of unknown etiology that affects mainly women between 30 and 60 years old. It is characterized by the triad of multifocal scarring alopecia of the scalp, lichenoid follicular eruption and hypotrichosis of axillary and pubic regions. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. Therapy is a challenge, with frequent relapses after local and systemic treatments. We report a typical case of this rare syndrome in a male patient of 46 years.
publishDate 2014
dc.date.none.fl_str_mv 2014-09-19T00:00:00Z
dc.type.driver.fl_str_mv journal article
info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.29021/spdv.72.2.261
oai:ojs.revista.spdv.com.pt:article/261
url https://doi.org/10.29021/spdv.72.2.261
identifier_str_mv oai:ojs.revista.spdv.com.pt:article/261
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://revista.spdv.com.pt/index.php/spdv/article/view/261
https://doi.org/10.29021/spdv.72.2.261
https://revista.spdv.com.pt/index.php/spdv/article/view/261/236
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
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dc.publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
dc.source.none.fl_str_mv Journal of the Portuguese Society of Dermatology and Venereology; Vol 72 No 2 (2014): Abril - Junho; 233-235
Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 72 n. 2 (2014): Abril - Junho; 233-235
2182-2409
2182-2395
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
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