Two cases of dermatomyositis: so equal and so different
Main Author: | |
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Publication Date: | 2009 |
Other Authors: | |
Format: | Article |
Language: | por |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | https://revista.spmi.pt/index.php/rpmi/article/view/1404 |
Summary: | Dermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis. |
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Two cases of dermatomyositis: so equal and so differentDois casos de dermatomiosite: tão iguais e tão diferentesdermatomiositemiopatias inflamatóriasneoplasiaDermatomyositisinflammatory myopathysneoplasiaDermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis.A dermatomiosite é uma doença auto-imune multissistémica rara, cujas principais características clínicas são fraqueza muscular e exantema típico. Com os meios de tratamento actualmente disponíveis, a taxa de sobrevivência aos 5 anos é superior a 90%. Existe um grupo de doentes, no entanto, em que a dermatomiosite surge como síndrome paraneoplásica e, nestes, a resposta à terapêutica fica comprometida e o prognóstico mais reservado.Os autores apresentam os casos clínicos de dois doentes do sexo masculino de 68 anos de idade, com fraqueza muscular, disfagia e exantema cutâneo típico, mas com resposta ao tratamento e evolução clínica diferente e que espelham a influência que uma neoplasia subjacente pode ter na evolução da dermatomiosite.Sociedade Portuguesa de Medicina Interna2009-06-30info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://revista.spmi.pt/index.php/rpmi/article/view/1404Internal Medicine; Vol. 16 No. 2 (2009): Abril/ Junho; 117-123Medicina Interna; Vol. 16 N.º 2 (2009): Abril/ Junho; 117-1232183-99800872-671Xreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://revista.spmi.pt/index.php/rpmi/article/view/1404https://revista.spmi.pt/index.php/rpmi/article/view/1404/958Cardoso, Ana RitaGonçalves, Cristinainfo:eu-repo/semantics/openAccess2022-12-31T06:11:45Zoai:oai.revista.spmi.pt:article/1404Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:45:33.315764Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Two cases of dermatomyositis: so equal and so different Dois casos de dermatomiosite: tão iguais e tão diferentes |
title |
Two cases of dermatomyositis: so equal and so different |
spellingShingle |
Two cases of dermatomyositis: so equal and so different Cardoso, Ana Rita dermatomiosite miopatias inflamatórias neoplasia Dermatomyositis inflammatory myopathys neoplasia |
title_short |
Two cases of dermatomyositis: so equal and so different |
title_full |
Two cases of dermatomyositis: so equal and so different |
title_fullStr |
Two cases of dermatomyositis: so equal and so different |
title_full_unstemmed |
Two cases of dermatomyositis: so equal and so different |
title_sort |
Two cases of dermatomyositis: so equal and so different |
author |
Cardoso, Ana Rita |
author_facet |
Cardoso, Ana Rita Gonçalves, Cristina |
author_role |
author |
author2 |
Gonçalves, Cristina |
author2_role |
author |
dc.contributor.author.fl_str_mv |
Cardoso, Ana Rita Gonçalves, Cristina |
dc.subject.por.fl_str_mv |
dermatomiosite miopatias inflamatórias neoplasia Dermatomyositis inflammatory myopathys neoplasia |
topic |
dermatomiosite miopatias inflamatórias neoplasia Dermatomyositis inflammatory myopathys neoplasia |
description |
Dermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis. |
publishDate |
2009 |
dc.date.none.fl_str_mv |
2009-06-30 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://revista.spmi.pt/index.php/rpmi/article/view/1404 |
url |
https://revista.spmi.pt/index.php/rpmi/article/view/1404 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spmi.pt/index.php/rpmi/article/view/1404 https://revista.spmi.pt/index.php/rpmi/article/view/1404/958 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Medicina Interna |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Medicina Interna |
dc.source.none.fl_str_mv |
Internal Medicine; Vol. 16 No. 2 (2009): Abril/ Junho; 117-123 Medicina Interna; Vol. 16 N.º 2 (2009): Abril/ Junho; 117-123 2183-9980 0872-671X reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
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FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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RCAAP |
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RCAAP |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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