Two cases of dermatomyositis: so equal and so different

Bibliographic Details
Main Author: Cardoso, Ana Rita
Publication Date: 2009
Other Authors: Gonçalves, Cristina
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://revista.spmi.pt/index.php/rpmi/article/view/1404
Summary: Dermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis.
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spelling Two cases of dermatomyositis: so equal and so differentDois casos de dermatomiosite: tão iguais e tão diferentesdermatomiositemiopatias inflamatóriasneoplasiaDermatomyositisinflammatory myopathysneoplasiaDermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis.A dermatomiosite é uma doença auto-imune multissistémica rara, cujas principais características clínicas são fraqueza muscular e exantema típico. Com os meios de tratamento actualmente disponíveis, a taxa de sobrevivência aos 5 anos é superior a 90%. Existe um grupo de doentes, no entanto, em que a dermatomiosite surge como síndrome paraneoplásica e, nestes, a resposta à terapêutica fica comprometida e o prognóstico mais reservado.Os autores apresentam os casos clínicos de dois doentes do sexo masculino de 68 anos de idade, com fraqueza muscular, disfagia e exantema cutâneo típico, mas com resposta ao tratamento e evolução clínica diferente e que espelham a influência que uma neoplasia subjacente pode ter na evolução da dermatomiosite.Sociedade Portuguesa de Medicina Interna2009-06-30info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://revista.spmi.pt/index.php/rpmi/article/view/1404Internal Medicine; Vol. 16 No. 2 (2009): Abril/ Junho; 117-123Medicina Interna; Vol. 16 N.º 2 (2009): Abril/ Junho; 117-1232183-99800872-671Xreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://revista.spmi.pt/index.php/rpmi/article/view/1404https://revista.spmi.pt/index.php/rpmi/article/view/1404/958Cardoso, Ana RitaGonçalves, Cristinainfo:eu-repo/semantics/openAccess2022-12-31T06:11:45Zoai:oai.revista.spmi.pt:article/1404Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:45:33.315764Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Two cases of dermatomyositis: so equal and so different
Dois casos de dermatomiosite: tão iguais e tão diferentes
title Two cases of dermatomyositis: so equal and so different
spellingShingle Two cases of dermatomyositis: so equal and so different
Cardoso, Ana Rita
dermatomiosite
miopatias inflamatórias
neoplasia
Dermatomyositis
inflammatory myopathys
neoplasia
title_short Two cases of dermatomyositis: so equal and so different
title_full Two cases of dermatomyositis: so equal and so different
title_fullStr Two cases of dermatomyositis: so equal and so different
title_full_unstemmed Two cases of dermatomyositis: so equal and so different
title_sort Two cases of dermatomyositis: so equal and so different
author Cardoso, Ana Rita
author_facet Cardoso, Ana Rita
Gonçalves, Cristina
author_role author
author2 Gonçalves, Cristina
author2_role author
dc.contributor.author.fl_str_mv Cardoso, Ana Rita
Gonçalves, Cristina
dc.subject.por.fl_str_mv dermatomiosite
miopatias inflamatórias
neoplasia
Dermatomyositis
inflammatory myopathys
neoplasia
topic dermatomiosite
miopatias inflamatórias
neoplasia
Dermatomyositis
inflammatory myopathys
neoplasia
description Dermatomyositis is a rare systemic autoimmune disease, which usually presents with muscular weakness and typical rash. With adequate treatment 90% of the patients are alive 5 years after the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one, the treatment response decreases and the prognosis is worse. The authors present clinical cases of two 68 year old men, with muscular weakness, dysphagia and typical rash, but with different treatment response and clinical results which mirrored the influence of an associated neoplastic disease on the course of dermatomyositis.
publishDate 2009
dc.date.none.fl_str_mv 2009-06-30
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dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
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dc.identifier.uri.fl_str_mv https://revista.spmi.pt/index.php/rpmi/article/view/1404
url https://revista.spmi.pt/index.php/rpmi/article/view/1404
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://revista.spmi.pt/index.php/rpmi/article/view/1404
https://revista.spmi.pt/index.php/rpmi/article/view/1404/958
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dc.publisher.none.fl_str_mv Sociedade Portuguesa de Medicina Interna
publisher.none.fl_str_mv Sociedade Portuguesa de Medicina Interna
dc.source.none.fl_str_mv Internal Medicine; Vol. 16 No. 2 (2009): Abril/ Junho; 117-123
Medicina Interna; Vol. 16 N.º 2 (2009): Abril/ Junho; 117-123
2183-9980
0872-671X
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