Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity

Bibliographic Details
Main Author: Pedrosa Rocha, Gustavo
Publication Date: 2024
Other Authors: Trindade Soares, Mafalda, Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal., Saraiva, Marlene, Matos, Catarina, Freire, Filipe
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.29315/gm.v11i4.810
Summary: Ramsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact.
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spelling Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary EntitySíndrome de Ramsay-Hunt com Polineuropatia Craniana e Disfagia Grave: Uma Entidade Rara e MultidisciplinarCranial Nerve DiseasesCranial NervesFacial ParalysisHerpes Zoster OticusDoenças dos Nervos CranianosHerpes Zoster OticusNervos CranianosParalisia FacialRamsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact.A síndrome de Ramsay-Hunt (SRH) caracteriza-se como uma infeção do gânglio geniculado do nervo facial pelo vírus varicella zoster (VVZ) e apresenta-se pela tríada de otalgia, erupção vesicular da concha auricular e paralisia facial periférica ipsilateral. O envolvimento de outros pares cranianos é raro, mas pode trazer dificuldade e atraso diagnóstico e um mau prognóstico.Apresentamos o caso de um doente com SRH e extensão a polineuropatia afetando o V, VII, VIII, IX e X pares cranianos e consequente sintomatologia que motivou internamento hospitalar prolongado e uma abordagem multidisciplinar de diferentes especialidades médicas. Apesar do mau prognóstico, apresentou uma significativa recuperação clínica e radiológica.A prevenção e a atenuação do VVZ e das suas complicações são cada vez mais possíveis e o aumento do conhecimento sobre a doença para a população e para os clínicos poderá ter impacto significativo.CUF Academic Center2024-12-27info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.29315/gm.v11i4.810https://doi.org/10.29315/gm.v11i4.810Gazeta Médica; NUMBER 4 · VOLUME 11 · OCTOBER/DECEMBER 2024; 326-330Gazeta Médica; NÚMERO 4 · VOLUME 11 · OUTUBRO/DEZEMBRO 2024; 326-3302184-06282183-813510.29315/gm.v11i4reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://www.gazetamedica.pt/index.php/gazeta/article/view/810https://www.gazetamedica.pt/index.php/gazeta/article/view/810/522Copyright (c) 2015 Gazeta Médicainfo:eu-repo/semantics/openAccessPedrosa Rocha, GustavoTrindade Soares, MafaldaDelgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal.Saraiva, MarleneMatos, CatarinaFreire, Filipe2024-12-28T04:45:33Zoai:ojs.pkp.sfu.ca:article/810Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T18:54:06.556498Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
Síndrome de Ramsay-Hunt com Polineuropatia Craniana e Disfagia Grave: Uma Entidade Rara e Multidisciplinar
title Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
spellingShingle Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
Pedrosa Rocha, Gustavo
Cranial Nerve Diseases
Cranial Nerves
Facial Paralysis
Herpes Zoster Oticus
Doenças dos Nervos Cranianos
Herpes Zoster Oticus
Nervos Cranianos
Paralisia Facial
title_short Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
title_full Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
title_fullStr Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
title_full_unstemmed Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
title_sort Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
author Pedrosa Rocha, Gustavo
author_facet Pedrosa Rocha, Gustavo
Trindade Soares, Mafalda
Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal.
Saraiva, Marlene
Matos, Catarina
Freire, Filipe
author_role author
author2 Trindade Soares, Mafalda
Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal.
Saraiva, Marlene
Matos, Catarina
Freire, Filipe
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Pedrosa Rocha, Gustavo
Trindade Soares, Mafalda
Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal.
Saraiva, Marlene
Matos, Catarina
Freire, Filipe
dc.subject.por.fl_str_mv Cranial Nerve Diseases
Cranial Nerves
Facial Paralysis
Herpes Zoster Oticus
Doenças dos Nervos Cranianos
Herpes Zoster Oticus
Nervos Cranianos
Paralisia Facial
topic Cranial Nerve Diseases
Cranial Nerves
Facial Paralysis
Herpes Zoster Oticus
Doenças dos Nervos Cranianos
Herpes Zoster Oticus
Nervos Cranianos
Paralisia Facial
description Ramsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact.
publishDate 2024
dc.date.none.fl_str_mv 2024-12-27
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.29315/gm.v11i4.810
https://doi.org/10.29315/gm.v11i4.810
url https://doi.org/10.29315/gm.v11i4.810
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://www.gazetamedica.pt/index.php/gazeta/article/view/810
https://www.gazetamedica.pt/index.php/gazeta/article/view/810/522
dc.rights.driver.fl_str_mv Copyright (c) 2015 Gazeta Médica
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2015 Gazeta Médica
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv CUF Academic Center
publisher.none.fl_str_mv CUF Academic Center
dc.source.none.fl_str_mv Gazeta Médica; NUMBER 4 · VOLUME 11 · OCTOBER/DECEMBER 2024; 326-330
Gazeta Médica; NÚMERO 4 · VOLUME 11 · OUTUBRO/DEZEMBRO 2024; 326-330
2184-0628
2183-8135
10.29315/gm.v11i4
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reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
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