Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity
Main Author: | |
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Publication Date: | 2024 |
Other Authors: | , , , , |
Format: | Article |
Language: | por |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | https://doi.org/10.29315/gm.v11i4.810 |
Summary: | Ramsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact. |
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Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary EntitySíndrome de Ramsay-Hunt com Polineuropatia Craniana e Disfagia Grave: Uma Entidade Rara e MultidisciplinarCranial Nerve DiseasesCranial NervesFacial ParalysisHerpes Zoster OticusDoenças dos Nervos CranianosHerpes Zoster OticusNervos CranianosParalisia FacialRamsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact.A síndrome de Ramsay-Hunt (SRH) caracteriza-se como uma infeção do gânglio geniculado do nervo facial pelo vírus varicella zoster (VVZ) e apresenta-se pela tríada de otalgia, erupção vesicular da concha auricular e paralisia facial periférica ipsilateral. O envolvimento de outros pares cranianos é raro, mas pode trazer dificuldade e atraso diagnóstico e um mau prognóstico.Apresentamos o caso de um doente com SRH e extensão a polineuropatia afetando o V, VII, VIII, IX e X pares cranianos e consequente sintomatologia que motivou internamento hospitalar prolongado e uma abordagem multidisciplinar de diferentes especialidades médicas. Apesar do mau prognóstico, apresentou uma significativa recuperação clínica e radiológica.A prevenção e a atenuação do VVZ e das suas complicações são cada vez mais possíveis e o aumento do conhecimento sobre a doença para a população e para os clínicos poderá ter impacto significativo.CUF Academic Center2024-12-27info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.29315/gm.v11i4.810https://doi.org/10.29315/gm.v11i4.810Gazeta Médica; NUMBER 4 · VOLUME 11 · OCTOBER/DECEMBER 2024; 326-330Gazeta Médica; NÚMERO 4 · VOLUME 11 · OUTUBRO/DEZEMBRO 2024; 326-3302184-06282183-813510.29315/gm.v11i4reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://www.gazetamedica.pt/index.php/gazeta/article/view/810https://www.gazetamedica.pt/index.php/gazeta/article/view/810/522Copyright (c) 2015 Gazeta Médicainfo:eu-repo/semantics/openAccessPedrosa Rocha, GustavoTrindade Soares, MafaldaDelgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal.Saraiva, MarleneMatos, CatarinaFreire, Filipe2024-12-28T04:45:33Zoai:ojs.pkp.sfu.ca:article/810Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T18:54:06.556498Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity Síndrome de Ramsay-Hunt com Polineuropatia Craniana e Disfagia Grave: Uma Entidade Rara e Multidisciplinar |
title |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
spellingShingle |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity Pedrosa Rocha, Gustavo Cranial Nerve Diseases Cranial Nerves Facial Paralysis Herpes Zoster Oticus Doenças dos Nervos Cranianos Herpes Zoster Oticus Nervos Cranianos Paralisia Facial |
title_short |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
title_full |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
title_fullStr |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
title_full_unstemmed |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
title_sort |
Ramsay-Hunt Syndrome with Cranial Polyneuropathy and Severe Dysphagia: A Rare and Multidisciplinary Entity |
author |
Pedrosa Rocha, Gustavo |
author_facet |
Pedrosa Rocha, Gustavo Trindade Soares, Mafalda Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal. Saraiva, Marlene Matos, Catarina Freire, Filipe |
author_role |
author |
author2 |
Trindade Soares, Mafalda Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal. Saraiva, Marlene Matos, Catarina Freire, Filipe |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Pedrosa Rocha, Gustavo Trindade Soares, Mafalda Delgado, Serviço de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Hospital Prof. Doutor Fernando da Fonseca, Amadora, Portugal. Saraiva, Marlene Matos, Catarina Freire, Filipe |
dc.subject.por.fl_str_mv |
Cranial Nerve Diseases Cranial Nerves Facial Paralysis Herpes Zoster Oticus Doenças dos Nervos Cranianos Herpes Zoster Oticus Nervos Cranianos Paralisia Facial |
topic |
Cranial Nerve Diseases Cranial Nerves Facial Paralysis Herpes Zoster Oticus Doenças dos Nervos Cranianos Herpes Zoster Oticus Nervos Cranianos Paralisia Facial |
description |
Ramsay-Hunt syndrome is defined by varicella-zoster virus (VZV) reactivation in the geniculate ganglion of the facial nerve and its presentation involves otalgia, vesicular lesions of the outer ear and ipsilateral facial paralysis. Cranial polyneuropathy extension is rare, can sometimes take a challenging and delayed diagnosis and poor prognosis.We illustrate a case of varicella zoster virus cranial polyneuropathy affecting V, VII, VIII, IX and X cranial nerves and consequent symptomatology that led to prolonged hospitalization with multidisciplinary approach. Despite the poor prognosis, the patient had a significant clinical and imagiological improvement. Prevention and attenuation of VZV and its complications are becoming increasingly possible and the increase in knowledge about this disease for the population and physicians can have a significant impact. |
publishDate |
2024 |
dc.date.none.fl_str_mv |
2024-12-27 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29315/gm.v11i4.810 https://doi.org/10.29315/gm.v11i4.810 |
url |
https://doi.org/10.29315/gm.v11i4.810 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://www.gazetamedica.pt/index.php/gazeta/article/view/810 https://www.gazetamedica.pt/index.php/gazeta/article/view/810/522 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2015 Gazeta Médica info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2015 Gazeta Médica |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
CUF Academic Center |
publisher.none.fl_str_mv |
CUF Academic Center |
dc.source.none.fl_str_mv |
Gazeta Médica; NUMBER 4 · VOLUME 11 · OCTOBER/DECEMBER 2024; 326-330 Gazeta Médica; NÚMERO 4 · VOLUME 11 · OUTUBRO/DEZEMBRO 2024; 326-330 2184-0628 2183-8135 10.29315/gm.v11i4 reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
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FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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RCAAP |
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RCAAP |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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