Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects
Main Author: | |
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Publication Date: | 2009 |
Other Authors: | , , , , , , , |
Language: | eng |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | http://hdl.handle.net/10400.21/288 |
Summary: | The deposition of amyloid fibers at the peripheral nervous system can induce motor neuropathy in Familial Amiloidotic Polyneuropethy (FAP) patients. This produces progressive reductions in functional capacity. The only treatment for FAP is a liver transplant, followed by aggressive medication that can affect patients' metabolism. To our knowledge, there are no data on body fat distribution or comparison between healthy and FAP subjects, which may be important for clinical assessment and management of this disease. |
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Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjectsFisioterapiaReabilitaçãoPolineuropatia amiloidótica familiarGordura corporalThe deposition of amyloid fibers at the peripheral nervous system can induce motor neuropathy in Familial Amiloidotic Polyneuropethy (FAP) patients. This produces progressive reductions in functional capacity. The only treatment for FAP is a liver transplant, followed by aggressive medication that can affect patients' metabolism. To our knowledge, there are no data on body fat distribution or comparison between healthy and FAP subjects, which may be important for clinical assessment and management of this disease.American College of Sports MedicineRCIPLPimenta, NunoSanta-Clara, HelenaTomás, Maria TeresaMonteiro, EstelaCabri, JanFreire, AntónioBarroso, EduardoSardinha, LuísFernhall, Bo2011-11-09T09:31:09Z2009-052009-05-01T00:00:00Zconference objectinfo:eu-repo/semantics/publishedVersionapplication/pdfhttp://hdl.handle.net/10400.21/288enginfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2025-02-12T09:06:27Zoai:repositorio.ipl.pt:10400.21/288Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T19:58:41.228082Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
title |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
spellingShingle |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects Pimenta, Nuno Fisioterapia Reabilitação Polineuropatia amiloidótica familiar Gordura corporal |
title_short |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
title_full |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
title_fullStr |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
title_full_unstemmed |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
title_sort |
Comparison of body fat content and distribution of familial amyloidotic polyneuropathy patients versus healthy subjects |
author |
Pimenta, Nuno |
author_facet |
Pimenta, Nuno Santa-Clara, Helena Tomás, Maria Teresa Monteiro, Estela Cabri, Jan Freire, António Barroso, Eduardo Sardinha, Luís Fernhall, Bo |
author_role |
author |
author2 |
Santa-Clara, Helena Tomás, Maria Teresa Monteiro, Estela Cabri, Jan Freire, António Barroso, Eduardo Sardinha, Luís Fernhall, Bo |
author2_role |
author author author author author author author author |
dc.contributor.none.fl_str_mv |
RCIPL |
dc.contributor.author.fl_str_mv |
Pimenta, Nuno Santa-Clara, Helena Tomás, Maria Teresa Monteiro, Estela Cabri, Jan Freire, António Barroso, Eduardo Sardinha, Luís Fernhall, Bo |
dc.subject.por.fl_str_mv |
Fisioterapia Reabilitação Polineuropatia amiloidótica familiar Gordura corporal |
topic |
Fisioterapia Reabilitação Polineuropatia amiloidótica familiar Gordura corporal |
description |
The deposition of amyloid fibers at the peripheral nervous system can induce motor neuropathy in Familial Amiloidotic Polyneuropethy (FAP) patients. This produces progressive reductions in functional capacity. The only treatment for FAP is a liver transplant, followed by aggressive medication that can affect patients' metabolism. To our knowledge, there are no data on body fat distribution or comparison between healthy and FAP subjects, which may be important for clinical assessment and management of this disease. |
publishDate |
2009 |
dc.date.none.fl_str_mv |
2009-05 2009-05-01T00:00:00Z 2011-11-09T09:31:09Z |
dc.type.driver.fl_str_mv |
conference object |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.21/288 |
url |
http://hdl.handle.net/10400.21/288 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
American College of Sports Medicine |
publisher.none.fl_str_mv |
American College of Sports Medicine |
dc.source.none.fl_str_mv |
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RCAAP |
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RCAAP |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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