Pregnancy in Marfan Syndrome – Two Case Reports

Detalhes bibliográficos
Autor(a) principal: Isidro Amaral, P
Data de Publicação: 2016
Outros Autores: Campos, A, Patrício, L
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Texto Completo: http://hdl.handle.net/10400.17/4154
Resumo: Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics.
id RCAP_5a0c37025b3bf21d237d9f66f563426f
oai_identifier_str oai:repositorio.chlc.pt:10400.17/4154
network_acronym_str RCAP
network_name_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository_id_str https://opendoar.ac.uk/repository/7160
spelling Pregnancy in Marfan Syndrome – Two Case ReportsGravidez na Síndrome de Marfan – dois casos clínicosMarfan SyndromePregnancyAortic dilatationMAC OBSMarfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics.Federação das Sociedades Portuguesas de Obstetrícia e GinecologiaRepositório da Unidade Local de Saúde São JoséIsidro Amaral, PCampos, APatrício, L2022-07-28T09:16:17Z20162016-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/4154porinfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2025-03-06T16:50:13Zoai:repositorio.chlc.pt:10400.17/4154Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-29T00:21:07.983246Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Pregnancy in Marfan Syndrome – Two Case Reports
Gravidez na Síndrome de Marfan – dois casos clínicos
title Pregnancy in Marfan Syndrome – Two Case Reports
spellingShingle Pregnancy in Marfan Syndrome – Two Case Reports
Isidro Amaral, P
Marfan Syndrome
Pregnancy
Aortic dilatation
MAC OBS
title_short Pregnancy in Marfan Syndrome – Two Case Reports
title_full Pregnancy in Marfan Syndrome – Two Case Reports
title_fullStr Pregnancy in Marfan Syndrome – Two Case Reports
title_full_unstemmed Pregnancy in Marfan Syndrome – Two Case Reports
title_sort Pregnancy in Marfan Syndrome – Two Case Reports
author Isidro Amaral, P
author_facet Isidro Amaral, P
Campos, A
Patrício, L
author_role author
author2 Campos, A
Patrício, L
author2_role author
author
dc.contributor.none.fl_str_mv Repositório da Unidade Local de Saúde São José
dc.contributor.author.fl_str_mv Isidro Amaral, P
Campos, A
Patrício, L
dc.subject.por.fl_str_mv Marfan Syndrome
Pregnancy
Aortic dilatation
MAC OBS
topic Marfan Syndrome
Pregnancy
Aortic dilatation
MAC OBS
description Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics.
publishDate 2016
dc.date.none.fl_str_mv 2016
2016-01-01T00:00:00Z
2022-07-28T09:16:17Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/4154
url http://hdl.handle.net/10400.17/4154
dc.language.iso.fl_str_mv por
language por
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Federação das Sociedades Portuguesas de Obstetrícia e Ginecologia
publisher.none.fl_str_mv Federação das Sociedades Portuguesas de Obstetrícia e Ginecologia
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
_version_ 1833600498341511168

Registros relacionados