RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY

Bibliographic Details
Main Author: Vieira, Isabel
Publication Date: 2021
Other Authors: Dias, Emanuel, Borges, Lisa, Henrique, Alberto, Oliveira, Nelson, Cássio, Isabel
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.48750/acv.380
Summary: Cystic lymphangioma is a rare and benign malformation of the lymphatic system, with retroperitoneal location accounting for only 1% of all lymphangiomas. Clinical presentation is frequently nonspecific. Authors present a case report of a 38 years old woman with persistent abdominal pain refractory to treatment that required imaging investigation (abdominal ultrasound and thoraco-abdominopelvic computed tomography scan) unveiling a cystic retroperitoneal mass suggesting lymphangioma. Abdominal laparotomy was performed for complete excision of the tumor. Histopathological exam of surgical specimen confirmed the cystic lymphangioma diagnosis. Complete surgical excision is considered gold-standard therapy and allow definite diagnosis.
id RCAP_4c9e2bdd91e308ad880dec5fb5288c8c
oai_identifier_str oai:ojs.acvjournal.com:article/380
network_acronym_str RCAP
network_name_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository_id_str https://opendoar.ac.uk/repository/7160
spelling RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITYLINFANGIOMA CÍSTICO RETROPERITONEAL: CASO CLÍNICO DE UMA ENTIDADE CLÍNICA RARACystic lymphangiomaRetroperitoneumCystic abdominal massSurgical excisionLinfangioma císticoRetroperitonealMassa abdominal císticaExcisão cirúrgicaCystic lymphangioma is a rare and benign malformation of the lymphatic system, with retroperitoneal location accounting for only 1% of all lymphangiomas. Clinical presentation is frequently nonspecific. Authors present a case report of a 38 years old woman with persistent abdominal pain refractory to treatment that required imaging investigation (abdominal ultrasound and thoraco-abdominopelvic computed tomography scan) unveiling a cystic retroperitoneal mass suggesting lymphangioma. Abdominal laparotomy was performed for complete excision of the tumor. Histopathological exam of surgical specimen confirmed the cystic lymphangioma diagnosis. Complete surgical excision is considered gold-standard therapy and allow definite diagnosis.O linfangioma cístico é uma malformação benigna e rara do sistema linfático, cuja localização retroperitoneal corresponde a cerca de 1% de todos os linfangiomas. A sua apresentação clínica é frequentemente inespecífica. Os autores relatam o caso de uma mulher de 38 anos de idade com dor abdominal persistente e refratária à terapêutica médica, que por esse motivo realizou exames de imagem (ecografia abdominal e tomografia computadorizada toraco-abdomino- pélvica) que revelou uma imagem retroperitoneal de natureza cística, sugestiva de linfangioma. Foi proposta laparotomia para excisão completa da lesão. O exame histopatológico da peça operatória confirmou o diagnóstico de linfangioma cístico. A excisão cirúrgica completa é considerada a terapêutica de eleição, para além de permitir o diagnóstico definitivo.Sociedade Portuguesa de Angiologia e Cirurgia Vascular2021-06-03T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.48750/acv.380oai:ojs.acvjournal.com:article/380Angiologia e Cirurgia Vascular; Vol. 17 No. 1 (2021): March; 43-46Angiologia e Cirurgia Vascular; Vol. 17 N.º 1 (2021): Março; 43-462183-00961646-706Xreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttp://acvjournal.com/index.php/acv/article/view/380https://doi.org/10.48750/acv.380http://acvjournal.com/index.php/acv/article/view/380/233Copyright (c) 2021 Angiologia e Cirurgia Vascularinfo:eu-repo/semantics/openAccessVieira, IsabelDias, EmanuelBorges, LisaHenrique, AlbertoOliveira, NelsonCássio, Isabel2022-05-23T15:10:12Zoai:ojs.acvjournal.com:article/380Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T10:00:16.228864Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
LINFANGIOMA CÍSTICO RETROPERITONEAL: CASO CLÍNICO DE UMA ENTIDADE CLÍNICA RARA
title RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
spellingShingle RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
Vieira, Isabel
Cystic lymphangioma
Retroperitoneum
Cystic abdominal mass
Surgical excision
Linfangioma cístico
Retroperitoneal
Massa abdominal cística
Excisão cirúrgica
title_short RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
title_full RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
title_fullStr RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
title_full_unstemmed RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
title_sort RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY
author Vieira, Isabel
author_facet Vieira, Isabel
Dias, Emanuel
Borges, Lisa
Henrique, Alberto
Oliveira, Nelson
Cássio, Isabel
author_role author
author2 Dias, Emanuel
Borges, Lisa
Henrique, Alberto
Oliveira, Nelson
Cássio, Isabel
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Vieira, Isabel
Dias, Emanuel
Borges, Lisa
Henrique, Alberto
Oliveira, Nelson
Cássio, Isabel
dc.subject.por.fl_str_mv Cystic lymphangioma
Retroperitoneum
Cystic abdominal mass
Surgical excision
Linfangioma cístico
Retroperitoneal
Massa abdominal cística
Excisão cirúrgica
topic Cystic lymphangioma
Retroperitoneum
Cystic abdominal mass
Surgical excision
Linfangioma cístico
Retroperitoneal
Massa abdominal cística
Excisão cirúrgica
description Cystic lymphangioma is a rare and benign malformation of the lymphatic system, with retroperitoneal location accounting for only 1% of all lymphangiomas. Clinical presentation is frequently nonspecific. Authors present a case report of a 38 years old woman with persistent abdominal pain refractory to treatment that required imaging investigation (abdominal ultrasound and thoraco-abdominopelvic computed tomography scan) unveiling a cystic retroperitoneal mass suggesting lymphangioma. Abdominal laparotomy was performed for complete excision of the tumor. Histopathological exam of surgical specimen confirmed the cystic lymphangioma diagnosis. Complete surgical excision is considered gold-standard therapy and allow definite diagnosis.
publishDate 2021
dc.date.none.fl_str_mv 2021-06-03T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.48750/acv.380
oai:ojs.acvjournal.com:article/380
url https://doi.org/10.48750/acv.380
identifier_str_mv oai:ojs.acvjournal.com:article/380
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv http://acvjournal.com/index.php/acv/article/view/380
https://doi.org/10.48750/acv.380
http://acvjournal.com/index.php/acv/article/view/380/233
dc.rights.driver.fl_str_mv Copyright (c) 2021 Angiologia e Cirurgia Vascular
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2021 Angiologia e Cirurgia Vascular
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Angiologia e Cirurgia Vascular
publisher.none.fl_str_mv Sociedade Portuguesa de Angiologia e Cirurgia Vascular
dc.source.none.fl_str_mv Angiologia e Cirurgia Vascular; Vol. 17 No. 1 (2021): March; 43-46
Angiologia e Cirurgia Vascular; Vol. 17 N.º 1 (2021): Março; 43-46
2183-0096
1646-706X
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
_version_ 1833590353000660992