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Malignant eccrine porocarcinoma mimicking a parotid neoplasia

Bibliographic Details
Main Author: Carvalho, Miguel
Publication Date: 2020
Other Authors: Mourão, Márcia, Silva, Miguel, Amaral, Raul, Alves, António, Raposo, Sergio
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.34631/sporl.812
Summary: Introduction: Eccrine porocarcinoma is a rare malignant cutaneous neoplasia that arises from an eccrine sweat gland. Case report: We describe the clinical case of an 83-year-old man sent for observation by the Head and Neck Surgery group, presenting a painless, growing tumefaction of the right parotid region. The patient had been submitted to a cutaneous excisional biopsy of the same region 14 months before that revealed a squamous cell carcinoma. Managed as a parotid neoplasia, after appropriate diagnostic workup, a superficial parotidectomy was performed. The histopathological analysis revealed an eccrine porocarcinoma as the diagnosis. Discussion/Conclusion: An eccrine porocarcinoma does not have any clinicopathological specific criteria, and the histological analysis of a specimen frequently leads to diagnosis of a squamous cell carcinoma. With the description of this clinical case we aim to raise awareness of fellow ENT doctors to this rare entity, and substantiate the importance of a close relationship with the pathologist in minimizing misdiagnosis.
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spelling Malignant eccrine porocarcinoma mimicking a parotid neoplasiaPorocarcinoma écrino primário mimetizando neoplasia parotídeaparotid glandeccrine porocarcinomaporocarcinoma écrinoglândula parótidaIntroduction: Eccrine porocarcinoma is a rare malignant cutaneous neoplasia that arises from an eccrine sweat gland. Case report: We describe the clinical case of an 83-year-old man sent for observation by the Head and Neck Surgery group, presenting a painless, growing tumefaction of the right parotid region. The patient had been submitted to a cutaneous excisional biopsy of the same region 14 months before that revealed a squamous cell carcinoma. Managed as a parotid neoplasia, after appropriate diagnostic workup, a superficial parotidectomy was performed. The histopathological analysis revealed an eccrine porocarcinoma as the diagnosis. Discussion/Conclusion: An eccrine porocarcinoma does not have any clinicopathological specific criteria, and the histological analysis of a specimen frequently leads to diagnosis of a squamous cell carcinoma. With the description of this clinical case we aim to raise awareness of fellow ENT doctors to this rare entity, and substantiate the importance of a close relationship with the pathologist in minimizing misdiagnosis.Introdução: O porocarcinoma écrino é uma neoplasia cutânea maligna rara com origem nas glândulas sudoríparas écrinas. Caso clínico: Descrevemos o caso clínico de um doente de 83 anos encaminhado à consulta de Cirurgia de Cabeça e Pescoço por apresentar uma tumefação na região parotídea direita de crescimento lento e indolor. O doente havia sido submetido a biópsia excisional de carcinoma espinhocelular cutâneo da mesma região 14 meses antes. Tratado como portador de uma neoplasia parotídea, e após apropriado algoritmo diagnóstico, foi submetido a parotidectomia superficial. A análise histológica da peça operatória revelou um porocarcinoma écrino como diagnóstico definitivo. Discussão/Conclusão: O porocarcinoma écrino não apresenta critérios clinicopatológicos específicos, e a sua análise histológica leva frequentemente ao diagnóstico de carcinoma espinhocelular. A descrição deste caso visa alertar para uma entidade clínica com a qual a comunidade de otorrinolaringologistas tem um menor contacto, substanciando a importância de uma relação estreita com o patologista na diminuição de erros diagnósticos.Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço2020-08-12info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.34631/sporl.812https://doi.org/10.34631/sporl.812Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery; Vol. 58 No. 2 (2020): June; 81-85Revista Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço; Vol. 58 Núm. 2 (2020): Junho; 81-85Revista Portuguesa de Otorrinolaringologia-Cirurgia de Cabeça e Pescoço; Vol. 58 N.º 2 (2020): Junho; 81-852184-6499reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://journalsporl.com/index.php/sporl/article/view/2252https://journalsporl.com/index.php/sporl/article/view/2252/224Direitos de Autor (c) 2020 Revista Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoçoinfo:eu-repo/semantics/openAccessCarvalho, MiguelMourão, MárciaSilva, MiguelAmaral, RaulAlves, AntónioRaposo, Sergio2024-06-06T12:57:37Zoai:journalsporl.com:article/2252Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T17:53:34.833707Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Malignant eccrine porocarcinoma mimicking a parotid neoplasia
Porocarcinoma écrino primário mimetizando neoplasia parotídea
title Malignant eccrine porocarcinoma mimicking a parotid neoplasia
spellingShingle Malignant eccrine porocarcinoma mimicking a parotid neoplasia
Carvalho, Miguel
parotid gland
eccrine porocarcinoma
porocarcinoma écrino
glândula parótida
title_short Malignant eccrine porocarcinoma mimicking a parotid neoplasia
title_full Malignant eccrine porocarcinoma mimicking a parotid neoplasia
title_fullStr Malignant eccrine porocarcinoma mimicking a parotid neoplasia
title_full_unstemmed Malignant eccrine porocarcinoma mimicking a parotid neoplasia
title_sort Malignant eccrine porocarcinoma mimicking a parotid neoplasia
author Carvalho, Miguel
author_facet Carvalho, Miguel
Mourão, Márcia
Silva, Miguel
Amaral, Raul
Alves, António
Raposo, Sergio
author_role author
author2 Mourão, Márcia
Silva, Miguel
Amaral, Raul
Alves, António
Raposo, Sergio
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Carvalho, Miguel
Mourão, Márcia
Silva, Miguel
Amaral, Raul
Alves, António
Raposo, Sergio
dc.subject.por.fl_str_mv parotid gland
eccrine porocarcinoma
porocarcinoma écrino
glândula parótida
topic parotid gland
eccrine porocarcinoma
porocarcinoma écrino
glândula parótida
description Introduction: Eccrine porocarcinoma is a rare malignant cutaneous neoplasia that arises from an eccrine sweat gland. Case report: We describe the clinical case of an 83-year-old man sent for observation by the Head and Neck Surgery group, presenting a painless, growing tumefaction of the right parotid region. The patient had been submitted to a cutaneous excisional biopsy of the same region 14 months before that revealed a squamous cell carcinoma. Managed as a parotid neoplasia, after appropriate diagnostic workup, a superficial parotidectomy was performed. The histopathological analysis revealed an eccrine porocarcinoma as the diagnosis. Discussion/Conclusion: An eccrine porocarcinoma does not have any clinicopathological specific criteria, and the histological analysis of a specimen frequently leads to diagnosis of a squamous cell carcinoma. With the description of this clinical case we aim to raise awareness of fellow ENT doctors to this rare entity, and substantiate the importance of a close relationship with the pathologist in minimizing misdiagnosis.
publishDate 2020
dc.date.none.fl_str_mv 2020-08-12
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv https://doi.org/10.34631/sporl.812
https://doi.org/10.34631/sporl.812
url https://doi.org/10.34631/sporl.812
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language por
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https://journalsporl.com/index.php/sporl/article/view/2252/224
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dc.publisher.none.fl_str_mv Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
publisher.none.fl_str_mv Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
dc.source.none.fl_str_mv Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery; Vol. 58 No. 2 (2020): June; 81-85
Revista Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço; Vol. 58 Núm. 2 (2020): Junho; 81-85
Revista Portuguesa de Otorrinolaringologia-Cirurgia de Cabeça e Pescoço; Vol. 58 N.º 2 (2020): Junho; 81-85
2184-6499
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