Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária
Main Author: | |
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Publication Date: | 2007 |
Other Authors: | , , |
Format: | Article |
Language: | por |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | http://hdl.handle.net/10400.4/327 |
Summary: | Systemic Lupus Erythematosus (SLE) is a rheumatic autoimmune disease characterized by multisystemic involvement with a variable prognosis. The association with Antiphospholipid Syndrome (APS) occurs in about 36% of the patients, raising additional problems with treatment and monitoring of these patients. The authors report a clinical case of a girl with SLE and APS who represented Budd-Chiari Syndrome and severe thrombocytopenia. The patient had severe thrombotic event and simultaneously a high hemorrhagic risk due to thrombocytopenia. Long-term resolution of the thrombocytopenia was achieved with mycophenolate mofetil. Long-term anticoagulation for thrombosis prophylaxis is required |
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Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido SecundáriaBudd-Chiari syndrome and severe thrombocytopenia in a patient with Systemic Lupus Erythematosus and Secondary Antiphospholipid SyndromeLúpus Eritematoso SistémicoSíndrome AntifosfolipídicoSíndrome de Budd-ChiariTrombocitopeniaSystemic Lupus Erythematosus (SLE) is a rheumatic autoimmune disease characterized by multisystemic involvement with a variable prognosis. The association with Antiphospholipid Syndrome (APS) occurs in about 36% of the patients, raising additional problems with treatment and monitoring of these patients. The authors report a clinical case of a girl with SLE and APS who represented Budd-Chiari Syndrome and severe thrombocytopenia. The patient had severe thrombotic event and simultaneously a high hemorrhagic risk due to thrombocytopenia. Long-term resolution of the thrombocytopenia was achieved with mycophenolate mofetil. Long-term anticoagulation for thrombosis prophylaxis is requiredSociedade Portuguesa de ReumatologiaRIHUCDuarte, CCouto, MInês, LMalcata, AB2008-12-11T16:28:52Z20072007-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.4/327porinfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2025-01-30T03:20:54Zoai:rihuc.huc.min-saude.pt:10400.4/327Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T19:43:55.380567Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária Budd-Chiari syndrome and severe thrombocytopenia in a patient with Systemic Lupus Erythematosus and Secondary Antiphospholipid Syndrome |
title |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
spellingShingle |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária Duarte, C Lúpus Eritematoso Sistémico Síndrome Antifosfolipídico Síndrome de Budd-Chiari Trombocitopenia |
title_short |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
title_full |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
title_fullStr |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
title_full_unstemmed |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
title_sort |
Síndrome de Budd-Chiari e Trombocitopenia grave em doente com Lúpus Eritematoso Sistémico e Síndrome Antifosfolípido Secundária |
author |
Duarte, C |
author_facet |
Duarte, C Couto, M Inês, L Malcata, AB |
author_role |
author |
author2 |
Couto, M Inês, L Malcata, AB |
author2_role |
author author author |
dc.contributor.none.fl_str_mv |
RIHUC |
dc.contributor.author.fl_str_mv |
Duarte, C Couto, M Inês, L Malcata, AB |
dc.subject.por.fl_str_mv |
Lúpus Eritematoso Sistémico Síndrome Antifosfolipídico Síndrome de Budd-Chiari Trombocitopenia |
topic |
Lúpus Eritematoso Sistémico Síndrome Antifosfolipídico Síndrome de Budd-Chiari Trombocitopenia |
description |
Systemic Lupus Erythematosus (SLE) is a rheumatic autoimmune disease characterized by multisystemic involvement with a variable prognosis. The association with Antiphospholipid Syndrome (APS) occurs in about 36% of the patients, raising additional problems with treatment and monitoring of these patients. The authors report a clinical case of a girl with SLE and APS who represented Budd-Chiari Syndrome and severe thrombocytopenia. The patient had severe thrombotic event and simultaneously a high hemorrhagic risk due to thrombocytopenia. Long-term resolution of the thrombocytopenia was achieved with mycophenolate mofetil. Long-term anticoagulation for thrombosis prophylaxis is required |
publishDate |
2007 |
dc.date.none.fl_str_mv |
2007 2007-01-01T00:00:00Z 2008-12-11T16:28:52Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.4/327 |
url |
http://hdl.handle.net/10400.4/327 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Reumatologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Reumatologia |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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