Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case

Bibliographic Details
Main Author: Casas Novas, A.
Publication Date: 2010
Other Authors: Moreira, I., Brazão Santos, P., Monteiro, L.
Format: Article
Language: por
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.34631/sporl.271
Summary: Wegener's granulomatosis is a systemic disease of unknown ethiology, characterized by a clinical triad of paranasal sinus and nasal mucosa involvement, pulmonary infiltration and cavitation, and renal disease with hematuria. Wegener's granulomatosis usually affects young or middle-aged adults. Although is uncommon in children, patients can be affected at any age.We describe a clinical case of a 14-year-old girl presentation with epistaxis, subsequent investigation showed renal failure and multiple pulmonary nodules. A positive proteinase antineutrophilic cytoplasmic antibody test supported the diagnosis of Wegener's Granulomatosis, requiring dialysis and immunosupression. 
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spelling Epistaxis as first manifestation of Wegener's granulomatosis. Clinical caseEpistaxis como primeira manifestação de granulomatose Wegener. Caso clínicoepistaxisWegener's GranulomatosisvasculitisgranulomaepistaxisGranulomatose WegenervasculitegranulomaWegener's granulomatosis is a systemic disease of unknown ethiology, characterized by a clinical triad of paranasal sinus and nasal mucosa involvement, pulmonary infiltration and cavitation, and renal disease with hematuria. Wegener's granulomatosis usually affects young or middle-aged adults. Although is uncommon in children, patients can be affected at any age.We describe a clinical case of a 14-year-old girl presentation with epistaxis, subsequent investigation showed renal failure and multiple pulmonary nodules. A positive proteinase antineutrophilic cytoplasmic antibody test supported the diagnosis of Wegener's Granulomatosis, requiring dialysis and immunosupression. A Granulomatose de Wegener é uma doença sistémica de etiologia desconhecida, caracterizada pela tríade clínica: envolvimento da mucosa nasal e dos seios perinasais, infiltração e cavitação pulmonar e doença renal com hematúria. A Granulomatose de Wegener afecta normalmente adultos jovens e de meia idade e embora seja incomum nas crianças, pode surgir em qualquer estrato etário.Apresentamos o caso clínico de uma adolescente de 14 anos, com sintomas de epistaxis, cuja investigação posterior mostrou insuficiência renal e múltiplos nódulos pulmonares. O teste positivo para o anticorpo antineutrofílico citoplasmático suportou o diagnóstico de Granulomatose de Wegener, necessitando de terapêutica com hemodiálise e imunossupressão.Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço2010-06-27info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.34631/sporl.271https://doi.org/10.34631/sporl.271Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery; Vol. 48 No. 2 (2010): Junho; 89-92Revista Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço; Vol. 48 Núm. 2 (2010): Junho; 89-92Revista Portuguesa de Otorrinolaringologia-Cirurgia de Cabeça e Pescoço; Vol. 48 N.º 2 (2010): Junho; 89-922184-6499reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPporhttps://journalsporl.com/index.php/sporl/article/view/2466https://journalsporl.com/index.php/sporl/article/view/2466/471Casas Novas, A.Moreira, I.Brazão Santos, P.Monteiro, L.info:eu-repo/semantics/openAccess2024-06-06T12:58:41Zoai:journalsporl.com:article/2466Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T17:53:45.932742Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
Epistaxis como primeira manifestação de granulomatose Wegener. Caso clínico
title Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
spellingShingle Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
Casas Novas, A.
epistaxis
Wegener's Granulomatosis
vasculitis
granuloma
epistaxis
Granulomatose Wegener
vasculite
granuloma
title_short Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
title_full Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
title_fullStr Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
title_full_unstemmed Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
title_sort Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
author Casas Novas, A.
author_facet Casas Novas, A.
Moreira, I.
Brazão Santos, P.
Monteiro, L.
author_role author
author2 Moreira, I.
Brazão Santos, P.
Monteiro, L.
author2_role author
author
author
dc.contributor.author.fl_str_mv Casas Novas, A.
Moreira, I.
Brazão Santos, P.
Monteiro, L.
dc.subject.por.fl_str_mv epistaxis
Wegener's Granulomatosis
vasculitis
granuloma
epistaxis
Granulomatose Wegener
vasculite
granuloma
topic epistaxis
Wegener's Granulomatosis
vasculitis
granuloma
epistaxis
Granulomatose Wegener
vasculite
granuloma
description Wegener's granulomatosis is a systemic disease of unknown ethiology, characterized by a clinical triad of paranasal sinus and nasal mucosa involvement, pulmonary infiltration and cavitation, and renal disease with hematuria. Wegener's granulomatosis usually affects young or middle-aged adults. Although is uncommon in children, patients can be affected at any age.We describe a clinical case of a 14-year-old girl presentation with epistaxis, subsequent investigation showed renal failure and multiple pulmonary nodules. A positive proteinase antineutrophilic cytoplasmic antibody test supported the diagnosis of Wegener's Granulomatosis, requiring dialysis and immunosupression. 
publishDate 2010
dc.date.none.fl_str_mv 2010-06-27
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.34631/sporl.271
https://doi.org/10.34631/sporl.271
url https://doi.org/10.34631/sporl.271
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://journalsporl.com/index.php/sporl/article/view/2466
https://journalsporl.com/index.php/sporl/article/view/2466/471
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
publisher.none.fl_str_mv Sociedade Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço
dc.source.none.fl_str_mv Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery; Vol. 48 No. 2 (2010): Junho; 89-92
Revista Portuguesa de Otorrinolaringologia e Cirurgia de Cabeça e Pescoço; Vol. 48 Núm. 2 (2010): Junho; 89-92
Revista Portuguesa de Otorrinolaringologia-Cirurgia de Cabeça e Pescoço; Vol. 48 N.º 2 (2010): Junho; 89-92
2184-6499
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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