Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases
Main Author: | |
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Publication Date: | 2022 |
Other Authors: | , , , , , , |
Format: | Article |
Language: | eng |
Source: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Download full: | https://doi.org/10.25753/BirthGrowthMJ.v31.i2.25273 |
Summary: | Acute disseminated encephalomyelitis (ADEM) is an acute demyelinating disorder of the central nervous system. ADEM should be suspected when a patient develops multifocal neurologic abnormalities with encephalopathy, especially if occurring after a viral infection or immunization. In this study, the authors describe two cases of ADEM with positive anti-myelin oligodendrocyte glycoprotein (MOG) antibodies requiring hospitalization in a Pediatric Intensive Care Unit and plasmapheresis treatment. |
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Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical casesPlasmaferese na encefalomielite aguda disseminada associada a anticorpos anti-MOG – Dois casos clínicosCase ReportsAcute disseminated encephalomyelitis (ADEM) is an acute demyelinating disorder of the central nervous system. ADEM should be suspected when a patient develops multifocal neurologic abnormalities with encephalopathy, especially if occurring after a viral infection or immunization. In this study, the authors describe two cases of ADEM with positive anti-myelin oligodendrocyte glycoprotein (MOG) antibodies requiring hospitalization in a Pediatric Intensive Care Unit and plasmapheresis treatment.A encefalomielite aguda disseminada (ADEM) é uma doença desmielinizante aguda do sistema nervoso central. O diagnóstico de ADEM deve ser considerado quando o doente apresenta alterações neurológicas focais associadas a encefalopatia, sobretudo se as manifestações surgem após uma infeção vírica ou vacinação. Neste artigo, são descritos dois casos clínicos de ADEM com anticorpos anti-MOG positivos com necessidade de internamento em Unidade de Cuidados Intensivos Pediátricos e tratamento com plasmaferese.Unidade Local de Saúde de Santo António2022-06-30info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25753/BirthGrowthMJ.v31.i2.25273eng2183-9417Soares, JoanaFigueiredo, RafaelPinto, EduardaCardoso, Ana LúciaSarmento, AlziraSameiro Faria, MariaFigueiroa, SóniaFerreira, Paulainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-07T09:46:49Zoai:ojs.revistas.rcaap.pt:article/25273Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:39:46.469967Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases Plasmaferese na encefalomielite aguda disseminada associada a anticorpos anti-MOG – Dois casos clínicos |
title |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
spellingShingle |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases Soares, Joana Case Reports |
title_short |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
title_full |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
title_fullStr |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
title_full_unstemmed |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
title_sort |
Plasmapheresis in acute disseminated encephalomyelitis associated with anti-MOG antibodies – Two clinical cases |
author |
Soares, Joana |
author_facet |
Soares, Joana Figueiredo, Rafael Pinto, Eduarda Cardoso, Ana Lúcia Sarmento, Alzira Sameiro Faria, Maria Figueiroa, Sónia Ferreira, Paula |
author_role |
author |
author2 |
Figueiredo, Rafael Pinto, Eduarda Cardoso, Ana Lúcia Sarmento, Alzira Sameiro Faria, Maria Figueiroa, Sónia Ferreira, Paula |
author2_role |
author author author author author author author |
dc.contributor.author.fl_str_mv |
Soares, Joana Figueiredo, Rafael Pinto, Eduarda Cardoso, Ana Lúcia Sarmento, Alzira Sameiro Faria, Maria Figueiroa, Sónia Ferreira, Paula |
dc.subject.por.fl_str_mv |
Case Reports |
topic |
Case Reports |
description |
Acute disseminated encephalomyelitis (ADEM) is an acute demyelinating disorder of the central nervous system. ADEM should be suspected when a patient develops multifocal neurologic abnormalities with encephalopathy, especially if occurring after a viral infection or immunization. In this study, the authors describe two cases of ADEM with positive anti-myelin oligodendrocyte glycoprotein (MOG) antibodies requiring hospitalization in a Pediatric Intensive Care Unit and plasmapheresis treatment. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-06-30 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.25753/BirthGrowthMJ.v31.i2.25273 |
url |
https://doi.org/10.25753/BirthGrowthMJ.v31.i2.25273 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
2183-9417 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
Unidade Local de Saúde de Santo António |
publisher.none.fl_str_mv |
Unidade Local de Saúde de Santo António |
dc.source.none.fl_str_mv |
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FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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RCAAP |
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RCAAP |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
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