Turner Syndrome - an unusual cause for aortic dissection
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , , , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
Texto Completo: | http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
Resumo: | Abstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario. |
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Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
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spelling |
Turner Syndrome - an unusual cause for aortic dissectionTurner SyndromeAortic DissectionX ChromosomeBicuspid Aortic ValveCoarctationAbstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario.Sociedade Portuguesa de Angiologia e Cirurgia Vascular2020-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322Angiologia e Cirurgia Vascular v.16 n.4 2020reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322Augusto,RitaCampos,JacintaCoelho,AndreiaCoelho,NunoPinto,EveliseSemião,CarolinaRibeiro,JoãoBrandão,DanielCanedo,Alexandrainfo:eu-repo/semantics/openAccess2024-02-06T17:23:00Zoai:scielo:S1646-706X2020000400322Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T13:10:22.745889Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse |
dc.title.none.fl_str_mv |
Turner Syndrome - an unusual cause for aortic dissection |
title |
Turner Syndrome - an unusual cause for aortic dissection |
spellingShingle |
Turner Syndrome - an unusual cause for aortic dissection Augusto,Rita Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
title_short |
Turner Syndrome - an unusual cause for aortic dissection |
title_full |
Turner Syndrome - an unusual cause for aortic dissection |
title_fullStr |
Turner Syndrome - an unusual cause for aortic dissection |
title_full_unstemmed |
Turner Syndrome - an unusual cause for aortic dissection |
title_sort |
Turner Syndrome - an unusual cause for aortic dissection |
author |
Augusto,Rita |
author_facet |
Augusto,Rita Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
author_role |
author |
author2 |
Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
author2_role |
author author author author author author author author |
dc.contributor.author.fl_str_mv |
Augusto,Rita Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
dc.subject.por.fl_str_mv |
Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
topic |
Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
description |
Abstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-12-01 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
url |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Angiologia e Cirurgia Vascular |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Angiologia e Cirurgia Vascular |
dc.source.none.fl_str_mv |
Angiologia e Cirurgia Vascular v.16 n.4 2020 reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia instacron:RCAAP |
instname_str |
FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
collection |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) |
repository.name.fl_str_mv |
Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia |
repository.mail.fl_str_mv |
info@rcaap.pt |
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1833593502916673536 |