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Juvenile Dermatomyositis Forty Years On: Case Report

Bibliographic Details
Main Author: Rego de Figueiredo, I
Publication Date: 2018
Other Authors: Guerreiro Castro, S, Bernardino, V, Silva Nunes, J, Alves, P, Moraes-Fontes, MF
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: http://hdl.handle.net/10400.17/3086
Summary: We present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.
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spelling Juvenile Dermatomyositis Forty Years On: Case ReportCalcinosis/diagnosisCalcinosis/pathologyDermatomyositis/diagnosisDermatomyositis/pathologyHCC DAUTOIMHDE IMAHCC ENDDisease ProgressionInsulin ResistanceLipodystrophy/diagnosisLipodystrophy/pathologyMetabolic Syndrome/diagnosisMetabolic Syndrome/pathologyMuscular Atrophy/diagnosisMuscular Atrophy/pathologySeverity of Illness IndexWe present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.ElsevierRepositório da Unidade Local de Saúde São JoséRego de Figueiredo, IGuerreiro Castro, SBernardino, VSilva Nunes, JAlves, PMoraes-Fontes, MF2018-10-22T12:16:08Z20182018-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/3086eng10.1016/j.nmd.2018.06.011info:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2025-03-06T16:46:50Zoai:repositorio.chlc.pt:10400.17/3086Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-29T00:18:08.584447Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Juvenile Dermatomyositis Forty Years On: Case Report
title Juvenile Dermatomyositis Forty Years On: Case Report
spellingShingle Juvenile Dermatomyositis Forty Years On: Case Report
Rego de Figueiredo, I
Calcinosis/diagnosis
Calcinosis/pathology
Dermatomyositis/diagnosis
Dermatomyositis/pathology
HCC DAUTOIM
HDE IMA
HCC END
Disease Progression
Insulin Resistance
Lipodystrophy/diagnosis
Lipodystrophy/pathology
Metabolic Syndrome/diagnosis
Metabolic Syndrome/pathology
Muscular Atrophy/diagnosis
Muscular Atrophy/pathology
Severity of Illness Index
title_short Juvenile Dermatomyositis Forty Years On: Case Report
title_full Juvenile Dermatomyositis Forty Years On: Case Report
title_fullStr Juvenile Dermatomyositis Forty Years On: Case Report
title_full_unstemmed Juvenile Dermatomyositis Forty Years On: Case Report
title_sort Juvenile Dermatomyositis Forty Years On: Case Report
author Rego de Figueiredo, I
author_facet Rego de Figueiredo, I
Guerreiro Castro, S
Bernardino, V
Silva Nunes, J
Alves, P
Moraes-Fontes, MF
author_role author
author2 Guerreiro Castro, S
Bernardino, V
Silva Nunes, J
Alves, P
Moraes-Fontes, MF
author2_role author
author
author
author
author
dc.contributor.none.fl_str_mv Repositório da Unidade Local de Saúde São José
dc.contributor.author.fl_str_mv Rego de Figueiredo, I
Guerreiro Castro, S
Bernardino, V
Silva Nunes, J
Alves, P
Moraes-Fontes, MF
dc.subject.por.fl_str_mv Calcinosis/diagnosis
Calcinosis/pathology
Dermatomyositis/diagnosis
Dermatomyositis/pathology
HCC DAUTOIM
HDE IMA
HCC END
Disease Progression
Insulin Resistance
Lipodystrophy/diagnosis
Lipodystrophy/pathology
Metabolic Syndrome/diagnosis
Metabolic Syndrome/pathology
Muscular Atrophy/diagnosis
Muscular Atrophy/pathology
Severity of Illness Index
topic Calcinosis/diagnosis
Calcinosis/pathology
Dermatomyositis/diagnosis
Dermatomyositis/pathology
HCC DAUTOIM
HDE IMA
HCC END
Disease Progression
Insulin Resistance
Lipodystrophy/diagnosis
Lipodystrophy/pathology
Metabolic Syndrome/diagnosis
Metabolic Syndrome/pathology
Muscular Atrophy/diagnosis
Muscular Atrophy/pathology
Severity of Illness Index
description We present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.
publishDate 2018
dc.date.none.fl_str_mv 2018-10-22T12:16:08Z
2018
2018-01-01T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/3086
url http://hdl.handle.net/10400.17/3086
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1016/j.nmd.2018.06.011
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Elsevier
publisher.none.fl_str_mv Elsevier
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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