Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso

Bibliographic Details
Main Author: Piffer, Amanda de Queiroz
Publication Date: 2025
Other Authors: Domingues, Ana Victoria Carvalho, Porto, Letícia Iamada, Oliveira, Maria Amália Barbosa Duarte de, Tosello, Giuliano Tavares
Format: Article
Language: por
eng
spa
Source: Revista Brasileira de Cancerologia (Online)
Download full: https://rbc.inca.gov.br/index.php/revista/article/view/4762
Summary: Introduction:Primary malignant lesions of the vagina are atypical, and vaginal sarcomas are even more uncommon. Leiomyosarcomas represent less than 2% of gynecological malignancies, and only 10% of these occur outside the uterus. Case Report: Pregnant woman, 39 years old, sought medical attention due to pain and vaginal bleeding. A pregnant uterus and a solid vaginal mass extending into adjacent fat were found. At the 35th week of gestation, a cesarean section was performed with excision of the tumor, which was subsequently submitted to anatomopathological analysis and diagnosed as vaginal leiomyosarcoma. Conclusion: In this case, tumor removal was the chosen approach, given the presentation of the case, experience of the physicians involved, and availability of the hospital resources where the patient was treated. In fact, there are no specific guidelines for this type of presentation of vaginal leiomyosarcoma, which implies individualization of each case, with different therapeutic approaches, respecting the patient’s particularities.
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spelling Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de CasoLeiomiosarcoma de vagina en paciente embarazada: reporte de casoLeiomiossarcoma de Vagina em Paciente Gestante: Relato de CasoLeiomiossarcomaGravidezNeoplasias VaginaisHemorragia UterinaLeiomyosarcomaPregnancyVaginal NeoplasmsUterine HemorrhageLeiomiosarcomaEmbarazoNeoplasias VaginalesHemorragia UterinaIntroduction:Primary malignant lesions of the vagina are atypical, and vaginal sarcomas are even more uncommon. Leiomyosarcomas represent less than 2% of gynecological malignancies, and only 10% of these occur outside the uterus. Case Report: Pregnant woman, 39 years old, sought medical attention due to pain and vaginal bleeding. A pregnant uterus and a solid vaginal mass extending into adjacent fat were found. At the 35th week of gestation, a cesarean section was performed with excision of the tumor, which was subsequently submitted to anatomopathological analysis and diagnosed as vaginal leiomyosarcoma. Conclusion: In this case, tumor removal was the chosen approach, given the presentation of the case, experience of the physicians involved, and availability of the hospital resources where the patient was treated. In fact, there are no specific guidelines for this type of presentation of vaginal leiomyosarcoma, which implies individualization of each case, with different therapeutic approaches, respecting the patient’s particularities.Introducción: Las lesiones malignas primarias de la vagina son atípicas y los sarcomas vaginales son aún más infrecuentes. Los leiomiosarcomas representan menos del 2% de las neoplasias malignas ginecológicas y solo el 10% de ellas se produce fuera del útero. Informe del caso: Mujer de 39 años, embarazada, acudió al médico presentando dolor y sangrado vaginal. Se encontró un útero embarazado y una masa vaginal sólida que se extendía hacia la grasa adyacente. En la semana 35 de gestación se realizó cesárea con escisión del tumor, el cual posteriormente fue sometido a análisis anatomopatológico, siendo diagnosticado como leiomiosarcoma vaginal. Conclusión: La escisión del tumor, en este caso, fue el abordaje elegido teniendo en cuenta factores como la presentación del caso, la experiencia de los médicos involucrados y la disponibilidad de recursos en el hospital donde se trató a la paciente. De hecho, no existen pautas específicas para este tipo de presentación del leiomiosarcoma vaginal, lo que implica la individualización de cada caso, con abordajes terapéuticos variados, respetando las particularidades de cada paciente.Introdução: As lesões malignas primárias da vagina são atípicas, e sarcomas vaginais ainda mais incomuns. Leiomiossarcomas retratam menos de 2% das neoplasias malignas ginecológicas, e apenas 10% destes ocorrem fora do útero. Relato do caso: Mulher, 39 anos, gestante, procurou atendimento médico apresentando dor e sangramento vaginal. Foram constatados útero gravídico e massa sólida vaginal que se estendia para gordura adjacente. Na 35ª semana de gestação, foi realizada uma cesárea com exérese da tumoração que posteriormente foi submetida à análise anatomopatológica, sendo diagnosticada como leiomiossarcoma de vagina. Conclusão: A exérese da tumoração, neste caso, foi a abordagem escolhida levando em conta fatores como apresentação do caso, experiência dos médicos envolvidos e disponibilidade de recursos no hospital onde a paciente foi atendida. De fato, não há guidelines específicos para esse tipo de apresentação de leimiossarcoma vaginal, o que implica em individualização de cada caso, com condutas terapêuticas variadas, respeitando as particularidades de cada paciente.INCA2025-01-24info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfapplication/pdfapplication/pdftext/htmlhttps://rbc.inca.gov.br/index.php/revista/article/view/476210.32635/2176-9745.RBC.2024v70n4.4762Revista Brasileira de Cancerologia; Vol. 70 No. 4 (2024): oct./nov./dec.; e-214762Revista Brasileira de Cancerologia; Vol. 70 Núm. 4 (2024): oct./nov./dic.; e-214762Revista Brasileira de Cancerologia; v. 70 n. 4 (2024): out./nov./dez.; e-2147622176-97450034-7116reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporengspahttps://rbc.inca.gov.br/index.php/revista/article/view/4762/3744https://rbc.inca.gov.br/index.php/revista/article/view/4762/3745https://rbc.inca.gov.br/index.php/revista/article/view/4762/3746https://rbc.inca.gov.br/index.php/revista/article/view/4762/3775Copyright (c) 2025 Revista Brasileira de Cancerologiahttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccess Piffer, Amanda de QueirozDomingues, Ana Victoria CarvalhoPorto, Letícia Iamada Oliveira, Maria Amália Barbosa Duarte deTosello, Giuliano Tavares2025-01-29T18:48:00Zoai:rbc.inca.gov.br:article/4762Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2025-01-29T18:48Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
Leiomiosarcoma de vagina en paciente embarazada: reporte de caso
Leiomiossarcoma de Vagina em Paciente Gestante: Relato de Caso
title Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
spellingShingle Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
Piffer, Amanda de Queiroz
Leiomiossarcoma
Gravidez
Neoplasias Vaginais
Hemorragia Uterina
Leiomyosarcoma
Pregnancy
Vaginal Neoplasms
Uterine Hemorrhage
Leiomiosarcoma
Embarazo
Neoplasias Vaginales
Hemorragia Uterina
title_short Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
title_full Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
title_fullStr Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
title_full_unstemmed Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
title_sort Leiomiosarcoma de Vagina en Paciente Embarazada: Informe de Caso
author Piffer, Amanda de Queiroz
author_facet Piffer, Amanda de Queiroz
Domingues, Ana Victoria Carvalho
Porto, Letícia Iamada
Oliveira, Maria Amália Barbosa Duarte de
Tosello, Giuliano Tavares
author_role author
author2 Domingues, Ana Victoria Carvalho
Porto, Letícia Iamada
Oliveira, Maria Amália Barbosa Duarte de
Tosello, Giuliano Tavares
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Piffer, Amanda de Queiroz
Domingues, Ana Victoria Carvalho
Porto, Letícia Iamada
Oliveira, Maria Amália Barbosa Duarte de
Tosello, Giuliano Tavares
dc.subject.por.fl_str_mv Leiomiossarcoma
Gravidez
Neoplasias Vaginais
Hemorragia Uterina
Leiomyosarcoma
Pregnancy
Vaginal Neoplasms
Uterine Hemorrhage
Leiomiosarcoma
Embarazo
Neoplasias Vaginales
Hemorragia Uterina
topic Leiomiossarcoma
Gravidez
Neoplasias Vaginais
Hemorragia Uterina
Leiomyosarcoma
Pregnancy
Vaginal Neoplasms
Uterine Hemorrhage
Leiomiosarcoma
Embarazo
Neoplasias Vaginales
Hemorragia Uterina
description Introduction:Primary malignant lesions of the vagina are atypical, and vaginal sarcomas are even more uncommon. Leiomyosarcomas represent less than 2% of gynecological malignancies, and only 10% of these occur outside the uterus. Case Report: Pregnant woman, 39 years old, sought medical attention due to pain and vaginal bleeding. A pregnant uterus and a solid vaginal mass extending into adjacent fat were found. At the 35th week of gestation, a cesarean section was performed with excision of the tumor, which was subsequently submitted to anatomopathological analysis and diagnosed as vaginal leiomyosarcoma. Conclusion: In this case, tumor removal was the chosen approach, given the presentation of the case, experience of the physicians involved, and availability of the hospital resources where the patient was treated. In fact, there are no specific guidelines for this type of presentation of vaginal leiomyosarcoma, which implies individualization of each case, with different therapeutic approaches, respecting the patient’s particularities.
publishDate 2025
dc.date.none.fl_str_mv 2025-01-24
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Relato de Caso
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url https://rbc.inca.gov.br/index.php/revista/article/view/4762
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https://rbc.inca.gov.br/index.php/revista/article/view/4762/3746
https://rbc.inca.gov.br/index.php/revista/article/view/4762/3775
dc.rights.driver.fl_str_mv Copyright (c) 2025 Revista Brasileira de Cancerologia
https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2025 Revista Brasileira de Cancerologia
https://creativecommons.org/licenses/by/4.0
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application/pdf
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dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 70 No. 4 (2024): oct./nov./dec.; e-214762
Revista Brasileira de Cancerologia; Vol. 70 Núm. 4 (2024): oct./nov./dic.; e-214762
Revista Brasileira de Cancerologia; v. 70 n. 4 (2024): out./nov./dez.; e-214762
2176-9745
0034-7116
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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