A Rare Case of Bullous Pemphigoid in an Infant

Bibliographic Details
Main Author: Pinto, Ana Marcos-
Publication Date: 2021
Other Authors: Costin, Adelina, Bartolo, Elvira, Tapadinhas, Cristina
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://ojs.pjp.spp.pt/article/view/20477
Summary: Bullous pemphigoid is an autoimmune blistering skin disease, rare in infancy, but increasingly reported. We describe a case of bullous pemphigoid in a 6-month-old infant with an excellent response to topical and oral corticosteroids. In this age group, the dermatosis assumes some particularities which must be recognized by clinicians in order to prevent unnecessary diagnostic workup or diagnostic delay and treat appropriately to avoid severe morbidity.
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spelling A Rare Case of Bullous Pemphigoid in an InfantCase reportsBullous pemphigoid is an autoimmune blistering skin disease, rare in infancy, but increasingly reported. We describe a case of bullous pemphigoid in a 6-month-old infant with an excellent response to topical and oral corticosteroids. In this age group, the dermatosis assumes some particularities which must be recognized by clinicians in order to prevent unnecessary diagnostic workup or diagnostic delay and treat appropriately to avoid severe morbidity.O penfigóde bolhoso é uma doença autoimune da pele, rara na infância, mas cada vez mais descrita.  Descrevemos um caso de penfigoide bolhoso num bebé de 6 meses de idade com uma excelente resposta a corticosteroides tópicos e orais. Nesta faixa etária, a dermatose assume algumas particularidades que devem ser reconhecidas pelos clínicos, a fim de evitar a realização de exames complementares desnecessários ou o atraso no diagnóstico e tratar adequadamente para evitar morbilidade associada.Sociedade Portuguesa de Pediatria2021-04-15info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://ojs.pjp.spp.pt/article/view/20477eng2184-44532184-3333Pinto, Ana Marcos-Costin, AdelinaBartolo, ElviraTapadinhas, Cristinainfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2024-05-06T15:12:31Zoai:ojs.revistas.rcaap.pt:article/20477Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T14:38:43.701167Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv A Rare Case of Bullous Pemphigoid in an Infant
title A Rare Case of Bullous Pemphigoid in an Infant
spellingShingle A Rare Case of Bullous Pemphigoid in an Infant
Pinto, Ana Marcos-
Case reports
title_short A Rare Case of Bullous Pemphigoid in an Infant
title_full A Rare Case of Bullous Pemphigoid in an Infant
title_fullStr A Rare Case of Bullous Pemphigoid in an Infant
title_full_unstemmed A Rare Case of Bullous Pemphigoid in an Infant
title_sort A Rare Case of Bullous Pemphigoid in an Infant
author Pinto, Ana Marcos-
author_facet Pinto, Ana Marcos-
Costin, Adelina
Bartolo, Elvira
Tapadinhas, Cristina
author_role author
author2 Costin, Adelina
Bartolo, Elvira
Tapadinhas, Cristina
author2_role author
author
author
dc.contributor.author.fl_str_mv Pinto, Ana Marcos-
Costin, Adelina
Bartolo, Elvira
Tapadinhas, Cristina
dc.subject.por.fl_str_mv Case reports
topic Case reports
description Bullous pemphigoid is an autoimmune blistering skin disease, rare in infancy, but increasingly reported. We describe a case of bullous pemphigoid in a 6-month-old infant with an excellent response to topical and oral corticosteroids. In this age group, the dermatosis assumes some particularities which must be recognized by clinicians in order to prevent unnecessary diagnostic workup or diagnostic delay and treat appropriately to avoid severe morbidity.
publishDate 2021
dc.date.none.fl_str_mv 2021-04-15
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://ojs.pjp.spp.pt/article/view/20477
url https://ojs.pjp.spp.pt/article/view/20477
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2184-4453
2184-3333
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
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reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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