Giant Intrathoracic Desmoid Tumor – a Case Report

Bibliographic Details
Main Author: Cunha, Sara
Publication Date: 2024
Other Authors: L. Graça, Luis, Lopes, Rita, Almeida, Vânia, Pancas, Rita
Format: Article
Language: eng
Source: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Download full: https://doi.org/10.48729/pjctvs.326
Summary: Desmoid tumors are soft tissue neoplasms arising from fascial and muscle-aponeurotic structure. These tumors are locally aggressive and have a high recurrence rate, even after complete resection. We present the case of a female with a giant intrathoracic desmoid tumor. She underwent complete surgical resection with no disease recurrence. Desmoid tumors’ natural history is not well defined and is often enigmatic, making these tumors difficult to manage. Currently, for intrathoracic desmoid tumors, medical treatment is the recommended approach, nevertheless, surgery can be considered in selected patients.
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spelling Giant Intrathoracic Desmoid Tumor – a Case ReportDesmoid TumorsDesmoid FibromatosisThoracic SurgeryDesmoid tumors are soft tissue neoplasms arising from fascial and muscle-aponeurotic structure. These tumors are locally aggressive and have a high recurrence rate, even after complete resection. We present the case of a female with a giant intrathoracic desmoid tumor. She underwent complete surgical resection with no disease recurrence. Desmoid tumors’ natural history is not well defined and is often enigmatic, making these tumors difficult to manage. Currently, for intrathoracic desmoid tumors, medical treatment is the recommended approach, nevertheless, surgery can be considered in selected patients.SOCIEDADE PORTUGUESA DE CIRURGIA CARDIO-TORÁCICA E VASCULAR2024-02-09info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.48729/pjctvs.326https://doi.org/10.48729/pjctvs.326Portuguese Journal of Cardiac Thoracic and Vascular Surgery; Vol. 30 No. 4 (2023): Oct-Dec; 63-662184-9927reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAPenghttps://pjctvs.com/index.php/journal/article/view/326https://pjctvs.com/index.php/journal/article/view/326/357Copyright (c) 2023 Portuguese Journal of Cardiac Thoracic and Vascular Surgeryinfo:eu-repo/semantics/openAccessCunha, SaraL. Graça, LuisLopes, RitaAlmeida, VâniaPancas, Rita2024-02-10T05:03:11Zoai:oai.pjctvs.com:article/326Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-28T13:21:27.224406Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Giant Intrathoracic Desmoid Tumor – a Case Report
title Giant Intrathoracic Desmoid Tumor – a Case Report
spellingShingle Giant Intrathoracic Desmoid Tumor – a Case Report
Cunha, Sara
Desmoid Tumors
Desmoid Fibromatosis
Thoracic Surgery
title_short Giant Intrathoracic Desmoid Tumor – a Case Report
title_full Giant Intrathoracic Desmoid Tumor – a Case Report
title_fullStr Giant Intrathoracic Desmoid Tumor – a Case Report
title_full_unstemmed Giant Intrathoracic Desmoid Tumor – a Case Report
title_sort Giant Intrathoracic Desmoid Tumor – a Case Report
author Cunha, Sara
author_facet Cunha, Sara
L. Graça, Luis
Lopes, Rita
Almeida, Vânia
Pancas, Rita
author_role author
author2 L. Graça, Luis
Lopes, Rita
Almeida, Vânia
Pancas, Rita
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Cunha, Sara
L. Graça, Luis
Lopes, Rita
Almeida, Vânia
Pancas, Rita
dc.subject.por.fl_str_mv Desmoid Tumors
Desmoid Fibromatosis
Thoracic Surgery
topic Desmoid Tumors
Desmoid Fibromatosis
Thoracic Surgery
description Desmoid tumors are soft tissue neoplasms arising from fascial and muscle-aponeurotic structure. These tumors are locally aggressive and have a high recurrence rate, even after complete resection. We present the case of a female with a giant intrathoracic desmoid tumor. She underwent complete surgical resection with no disease recurrence. Desmoid tumors’ natural history is not well defined and is often enigmatic, making these tumors difficult to manage. Currently, for intrathoracic desmoid tumors, medical treatment is the recommended approach, nevertheless, surgery can be considered in selected patients.
publishDate 2024
dc.date.none.fl_str_mv 2024-02-09
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.48729/pjctvs.326
https://doi.org/10.48729/pjctvs.326
url https://doi.org/10.48729/pjctvs.326
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://pjctvs.com/index.php/journal/article/view/326
https://pjctvs.com/index.php/journal/article/view/326/357
dc.rights.driver.fl_str_mv Copyright (c) 2023 Portuguese Journal of Cardiac Thoracic and Vascular Surgery
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2023 Portuguese Journal of Cardiac Thoracic and Vascular Surgery
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv SOCIEDADE PORTUGUESA DE CIRURGIA CARDIO-TORÁCICA E VASCULAR
publisher.none.fl_str_mv SOCIEDADE PORTUGUESA DE CIRURGIA CARDIO-TORÁCICA E VASCULAR
dc.source.none.fl_str_mv Portuguese Journal of Cardiac Thoracic and Vascular Surgery; Vol. 30 No. 4 (2023): Oct-Dec; 63-66
2184-9927
reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
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instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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