Short QT Syndrome Presenting As Syncope: How Short Is Too Short?

Detalhes bibliográficos
Autor(a) principal: Portugal, G
Data de Publicação: 2014
Outros Autores: Oliveira, MM, Silva Cunha, P, Filipa, F, Lousinha, A, Fiarresga, A, Nogueira da Silva, M, Cruz Ferreira, R
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
Texto Completo: http://hdl.handle.net/10400.17/1979
Resumo: We report the case of a 52-year-old man who presented to our emergency department (ED) after three episodes of syncope in the seven hours before admission. During his stay in the ED he had recurrent ventricular tachycardia (VT) requiring external electrical cardioversion. A 12-lead electrocardiogram (ECG) showed a short QT (SQT) interval (270 ms, QTc 327 ms), with frequent R-on-T extrasystoles triggering sustained polymorphic VT. After exclusion of other precipitating causes, the patient was diagnosed as having SQT syndrome (SQTS) according to the Gollob criteria. To our knowledge, this is the first known documentation of an SQT-caused arrhythmic episode on a 12-lead ECG, as well as the first reported case of SQTS in Portugal. The patient received an implantable cardioverter-defibrillator and was discharged. At a follow-up assessment 14 months later he was symptom-free, interrogation of the device showed no arrhythmic events, and the ECG showed a QT interval of 320 ms (QTc 347 ms).
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spelling Short QT Syndrome Presenting As Syncope: How Short Is Too Short?Quando o Intervalo QT é Curto Demais: Síncope Causada por Síndrome QT CurtoHSM CARSyncopeShort QT SyndromeSudden Cardiac DeathVentricular ArrhythmiaWe report the case of a 52-year-old man who presented to our emergency department (ED) after three episodes of syncope in the seven hours before admission. During his stay in the ED he had recurrent ventricular tachycardia (VT) requiring external electrical cardioversion. A 12-lead electrocardiogram (ECG) showed a short QT (SQT) interval (270 ms, QTc 327 ms), with frequent R-on-T extrasystoles triggering sustained polymorphic VT. After exclusion of other precipitating causes, the patient was diagnosed as having SQT syndrome (SQTS) according to the Gollob criteria. To our knowledge, this is the first known documentation of an SQT-caused arrhythmic episode on a 12-lead ECG, as well as the first reported case of SQTS in Portugal. The patient received an implantable cardioverter-defibrillator and was discharged. At a follow-up assessment 14 months later he was symptom-free, interrogation of the device showed no arrhythmic events, and the ECG showed a QT interval of 320 ms (QTc 347 ms).Sociedade Portuguesa de CardiologiaRepositório da Unidade Local de Saúde São JoséPortugal, GOliveira, MMSilva Cunha, PFilipa, FLousinha, AFiarresga, ANogueira da Silva, MCruz Ferreira, R2014-12-30T17:21:58Z20142014-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/1979enginfo:eu-repo/semantics/openAccessreponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiainstacron:RCAAP2025-03-06T16:46:39Zoai:repositorio.chlc.pt:10400.17/1979Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireinfo@rcaap.ptopendoar:https://opendoar.ac.uk/repository/71602025-05-29T00:17:36.510978Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologiafalse
dc.title.none.fl_str_mv Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
Quando o Intervalo QT é Curto Demais: Síncope Causada por Síndrome QT Curto
title Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
spellingShingle Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
Portugal, G
HSM CAR
Syncope
Short QT Syndrome
Sudden Cardiac Death
Ventricular Arrhythmia
title_short Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
title_full Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
title_fullStr Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
title_full_unstemmed Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
title_sort Short QT Syndrome Presenting As Syncope: How Short Is Too Short?
author Portugal, G
author_facet Portugal, G
Oliveira, MM
Silva Cunha, P
Filipa, F
Lousinha, A
Fiarresga, A
Nogueira da Silva, M
Cruz Ferreira, R
author_role author
author2 Oliveira, MM
Silva Cunha, P
Filipa, F
Lousinha, A
Fiarresga, A
Nogueira da Silva, M
Cruz Ferreira, R
author2_role author
author
author
author
author
author
author
dc.contributor.none.fl_str_mv Repositório da Unidade Local de Saúde São José
dc.contributor.author.fl_str_mv Portugal, G
Oliveira, MM
Silva Cunha, P
Filipa, F
Lousinha, A
Fiarresga, A
Nogueira da Silva, M
Cruz Ferreira, R
dc.subject.por.fl_str_mv HSM CAR
Syncope
Short QT Syndrome
Sudden Cardiac Death
Ventricular Arrhythmia
topic HSM CAR
Syncope
Short QT Syndrome
Sudden Cardiac Death
Ventricular Arrhythmia
description We report the case of a 52-year-old man who presented to our emergency department (ED) after three episodes of syncope in the seven hours before admission. During his stay in the ED he had recurrent ventricular tachycardia (VT) requiring external electrical cardioversion. A 12-lead electrocardiogram (ECG) showed a short QT (SQT) interval (270 ms, QTc 327 ms), with frequent R-on-T extrasystoles triggering sustained polymorphic VT. After exclusion of other precipitating causes, the patient was diagnosed as having SQT syndrome (SQTS) according to the Gollob criteria. To our knowledge, this is the first known documentation of an SQT-caused arrhythmic episode on a 12-lead ECG, as well as the first reported case of SQTS in Portugal. The patient received an implantable cardioverter-defibrillator and was discharged. At a follow-up assessment 14 months later he was symptom-free, interrogation of the device showed no arrhythmic events, and the ECG showed a QT interval of 320 ms (QTc 347 ms).
publishDate 2014
dc.date.none.fl_str_mv 2014-12-30T17:21:58Z
2014
2014-01-01T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/1979
url http://hdl.handle.net/10400.17/1979
dc.language.iso.fl_str_mv eng
language eng
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Cardiologia
publisher.none.fl_str_mv Sociedade Portuguesa de Cardiologia
dc.source.none.fl_str_mv reponame:Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
instname:FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron:RCAAP
instname_str FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
instacron_str RCAAP
institution RCAAP
reponame_str Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
collection Repositórios Científicos de Acesso Aberto de Portugal (RCAAP)
repository.name.fl_str_mv Repositórios Científicos de Acesso Aberto de Portugal (RCAAP) - FCCN, serviços digitais da FCT – Fundação para a Ciência e a Tecnologia
repository.mail.fl_str_mv info@rcaap.pt
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